From the Department of Anesthesiology, Sidra Medicine, Doha, Qatar.
CT Surgery Department, Hamad Medical Corporation, Doha, Qatar.
A A Pract. 2021 Mar 8;15(3):e01395. doi: 10.1213/XAA.0000000000001395.
Congenital methemoglobinemia is a rare disease that is easily overlooked in its mild form. It can lead to tissue hypoxia as methemoglobin does not possess oxygen-carrying capacity. Its management approach depends on the severity of the symptoms, methemoglobin level, and associated medical conditions. The perioperative management of congenital methemoglobinemia is well described in the literature; however, its management in children with congenital heart disease and undergoing cardiac surgery using cardiopulmonary bypass has not been reported. We present a case and its management where congenital methemoglobinemia was detected in the operating room in a child scheduled for cardiac surgery.
先天性高铁血红蛋白血症是一种罕见的疾病，在轻度形式下很容易被忽视。由于高铁血红蛋白没有携带氧气的能力，它会导致组织缺氧。其治疗方法取决于症状的严重程度、高铁血红蛋白水平和相关的医疗状况。先天性高铁血红蛋白血症的围手术期管理在文献中有详细描述；然而，在接受体外循环心脏手术的先天性心脏病儿童中，其管理尚未见报道。我们报告了一例在计划行心脏手术的儿童的手术室中发现先天性高铁血红蛋白血症的病例及其管理。
