Federal University of São Paulo (UNIFESP) - Paulista School of Medicine, Pediatric Oncology Institute - GRAACC/UNIFESP.
Departments of Surgery, Anesthesiology, & Pediatric Oncology, Boston Children's Hospital, Dana-Farber Cancer Institute, Harvard Medical School, 300 Longwood Ave, Fegan 3, Boston, MA 02115, USA.
Surg Oncol Clin N Am. 2021 Apr;30(2):275-290. doi: 10.1016/j.soc.2020.11.012. Epub 2021 Feb 3.
Pediatric adrenal tumors are uncommon entities that are frequently occult and identified incidentally or by recognizing symptoms related to hormone overproduction. They often have a genetic underpinning, arise from the medulla or cortex, can be malignant or benign, and require precise diagnostic algorithms. However, pseudotumors must also be a diagnostic consideration. Therapeutic interventions and plans are tumor dependent, but surgery is a cornerstone of treatment. Ongoing surveillance after treatment, regardless of malignant determination, is of utmost importance as well.
小儿肾上腺肿瘤是不常见的实体瘤，常为隐匿性，通过识别与激素过度产生相关的症状或偶然发现。它们通常有遗传基础，起源于髓质或皮质，可能是恶性或良性的，需要精确的诊断算法。然而，假性肿瘤也必须是一个诊断考虑因素。治疗干预和计划取决于肿瘤，但手术是治疗的基石。治疗后无论恶性程度如何，持续监测都非常重要。
