Department of Neurologic Surgery, Mayo Clinic, Rochester, Minnesota, USA,
Department of Pathology, Mayo Clinic, Rochester, Minnesota, USA.
Pediatr Neurosurg. 2021;56(2):157-162. doi: 10.1159/000511774. Epub 2021 Mar 12.
Infantile endodermal oculomotor nerve cyst (EONC) is an extremely rare entity. There are very few pediatric cases reported in the literature, and as expected, oculomotor palsy is the most common presenting symptom. To date however, the risk of recurrence of these lesions following surgical intervention is unclear due to a lack of long-term radiological follow-up.
We present a case of a 13-month-old male patient with an EONC and detail his surgical fenestration and postoperative course. Somewhat surprisingly, re-expansion occurred within 6 months and remained stable 2 years later.
A surgical approach to fenestration of an EONC in an infant is possible and should be performed by an expert neurosurgeon. Early recurrence is underreported in the current literature, and we encourage longer term radiological surveillance of these lesions after surgery to optimize primary and recurrent management in the future.
婴儿内胚层眼运动神经囊肿（EONC）是一种极为罕见的疾病。文献中仅报道过少数几例儿科病例，预计最常见的表现症状是眼运动神经瘫痪。然而，由于缺乏长期的影像学随访，目前尚不清楚这些病变在手术干预后是否有复发的风险。
我们报告了一例 13 个月大的男性 EONC 患者，并详细介绍了他的手术开窗术及术后过程。令人惊讶的是，6 个月内囊肿再次扩张，并在 2 年后保持稳定。
对婴儿的 EONC 进行开窗手术是可行的，应由专家神经外科医生进行。目前文献中对早期复发的报道较少，我们鼓励对这些术后病变进行更长时间的影像学监测，以便将来优化原发性和复发性病变的管理。
