Department of Respiratory Medicine, Saiseikai Yokohamashi Tobu Hospital, Japan.
Department of Diagnostic Pathology, Saiseikai Yokohamashi Tobu Hospital, Japan.
Intern Med. 2021 Oct 1;60(19):3137-3142. doi: 10.2169/internalmedicine.6456-20. Epub 2021 Mar 15.
Good's syndrome is associated with thymoma and acquired immunodeficiency. A 54-year-old man visited our hospital with a complaint of cough. Chest imaging revealed diffuse nodular shadows and anterior mediastinal mass. Hypogammaglobulinemia and a decreased B lymphocyte count were found by a laboratory evaluation. The lung nodules markedly regressed after immunoglobulin therapy. The mediastinal mass and remaining nodule were surgically resected and diagnosed as a type AB thymoma and a necrotizing epithelioid granuloma with T lymphocyte-dominant alveolitis, respectively. The overall appearances of these lesions were mostly in line with the spectrum of granulomatous-lymphocytic interstitial lung disease associated with Good's syndrome.
Good 综合征与胸腺瘤和获得性免疫缺陷相关。一位 54 岁男性因咳嗽就诊于我院。胸部影像学显示弥漫性结节影和前纵隔肿块。实验室检查发现低丙种球蛋白血症和 B 淋巴细胞计数减少。免疫球蛋白治疗后肺部结节明显消退。纵隔肿块和残余结节被手术切除,病理诊断分别为 AB 型胸腺瘤和伴有 T 淋巴细胞优势性肺泡炎的坏死性类上皮肉芽肿。这些病变的整体表现大多符合与 Good 综合征相关的肉芽肿性淋巴细胞性间质性肺病的谱。