Xie Tian-Hao, Ren Xiang-Xiang, Fu Yan, Ha Si-Ning, Liu Li-Tao, Jin Xiao-Shi
Department of General Surgery, Affiliated Hospital of Hebei University, Baoding 071000, Hebei Province, China.
Department of Ophthalmology, Baoding First Central Hospital, Baoding 071000, Hebei Province, China.
World J Clin Cases. 2021 Mar 6;9(7):1661-1667. doi: 10.12998/wjcc.v9.i7.1661.
Primary retroperitoneal liposarcoma (PRPLS) is a rare soft tissue tumor with nonspecific clinical symptoms; it has different computed tomography (CT) image features according to pathological types. Some patients with a single tumor have been previously reported in the literature. We present an exceptional case of a PRPLS patient with multiple large tumors exhibiting different patterns of appearance on CT and confirmed as atypical lipomatous tumor/well-differentiated liposarcoma by postoperative pathology.
A 64-year-old man presented with abdominal distension for 1 year. The patient was diagnosed with PRPLS based on physical examination, laparotomy, ultrasonography, CT scan, and surgery. Both of the tumors were completely resected through surgery and confirmed as atypical lipomatous tumor/well-differentiated liposarcoma by postoperative pathology. The postoperative course was uneventful without recurrence or metastasis, as demonstrated by abdominal-pelvic CT during an 18 mo follow-up.
Multiple large Well-differentiated liposarcomas with different patterns of appearance on CT image can occur simultaneously in the same patient, to which more attention should be paid to make an effective differential diagnosis.
原发性腹膜后脂肪肉瘤（PRPLS）是一种罕见的软组织肿瘤，临床症状不具特异性；根据病理类型不同，其计算机断层扫描（CT）图像特征各异。此前文献中曾报道过一些单发性肿瘤患者。我们报告一例特殊的PRPLS患者，其患有多个大肿瘤，CT表现出不同的形态，术后病理确诊为非典型脂肪瘤样肿瘤/高分化脂肪肉瘤。
一名64岁男性因腹胀1年就诊。通过体格检查、剖腹探查、超声检查、CT扫描及手术，该患者被诊断为PRPLS。两个肿瘤均通过手术完整切除，术后病理确诊为非典型脂肪瘤样肿瘤/高分化脂肪肉瘤。在18个月的随访期间，腹盆腔CT显示术后过程顺利，无复发或转移。
同一患者可同时出现多个在CT图像上表现出不同形态的大的高分化脂肪肉瘤，对此应予以更多关注以便进行有效的鉴别诊断。
