Department of Internal Medicine, Division of Rheumatology, University of Michigan, Ann Arbor, Michigan, USA.
Curr Opin Rheumatol. 2021 May 1;33(3):249-254. doi: 10.1097/BOR.0000000000000798.
Patients with symptomatic hypermobility syndrome such as hypermobile Ehlers-Danlos syndromes (hEDS) and hypermobility spectrum disorders (HSD) commonly present to rheumatologists with joint pain and functional disability. Providers often have difficulty with diagnosis due to a lack of knowledge on the range of associated manifestations and the available therapeutic modalities. This review will discuss recent updates on diagnostic measures and treatment options for rheumatologists to help patients navigate hEDS/HSD.
This article describes newer diagnostic measures and assessment of hEDS/HSD manifestations. Evidence supporting physical therapy and occupational therapy is provided, as well as recent updates on assistive devices, compressive garments, orthoses, and surgical interventions. Given patient heterogeneity specific guidance about the amount and type of therapies required to produce a beneficial effect is lacking. Treatment should be individualized, and many of the studies focus on regional joint complaints rather than a whole-body approach.
Physical therapy and occupational therapy remain the cornerstone of treatment.
患有症状性过度活动综合征（如 Ehlers-Danlos 高活动型综合征和高活动度谱系障碍）的患者常因关节疼痛和功能障碍而就诊于风湿病医生。由于对相关表现的范围和可用治疗方法缺乏了解，提供者在诊断方面常常存在困难。这篇综述将讨论诊断措施和治疗选择的最新更新，以帮助风湿病医生为患者提供导航 hEDS/HSD。
本文描述了 hEDS/HSD 表现的新的诊断措施和评估。提供了对物理治疗和职业治疗的证据支持，以及辅助设备、压缩服装、矫形器和手术干预的最新更新。鉴于患者的异质性，缺乏关于产生有益效果所需的治疗量和类型的具体指导。治疗应个体化，许多研究侧重于局部关节投诉，而不是全身方法。
物理治疗和职业治疗仍然是治疗的基石。
