Oka Satoshi, Ito Shu, Kai Takahiko, Hoshino Katsuomi, Watanabe Kazunori, Nakamura Jun, Abe Makoto, Watanabe Akinori
Department of Cardiology, Fujieda Municipal General Hospital, Japan.
Intern Med. 2021 Mar 22. doi: 10.2169/internalmedicine.7052-21.
Painful left bundle branch block (LBBB) syndrome is a rare disease that presents as simultaneous chest pain and transient LBBB without myocardial ischemia. We diagnosed a 72-year-old Japanese man with painful LBBB syndrome complicated by iron-overload cardiomyopathy. Phlebotomy was initially performed to improve myocardial iron deposition and conductive disturbance. Ironically, his chest pain was fully improved by the completion of incessant LBBB and walk-through phenomenon. However, this case demonstrates a clinically significant therapeutic strategy for cardiomyopathy-induced painful LBBB syndrome. Due to the lack of treatment guidelines, individualized treatment is required for each case of painful LBBB.
疼痛性左束支传导阻滞(LBBB)综合征是一种罕见疾病,表现为同时出现胸痛和短暂性LBBB且无心肌缺血。我们诊断出一名72岁的日本男性患有疼痛性LBBB综合征,并伴有铁过载性心肌病。最初进行了静脉放血以改善心肌铁沉积和传导障碍。具有讽刺意味的是,在持续性LBBB和贯穿现象完成后,他的胸痛完全缓解。然而,该病例展示了一种针对心肌病所致疼痛性LBBB综合征具有临床意义的治疗策略。由于缺乏治疗指南,对于每例疼痛性LBBB都需要个体化治疗。