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伴有铁过载心肌病的疼痛性左束支传导阻滞综合征

Painful Left Bundle Branch Block Syndrome Complicated by Iron-Overload Cardiomyopathy.

作者信息

Oka Satoshi, Ito Shu, Kai Takahiko, Hoshino Katsuomi, Watanabe Kazunori, Nakamura Jun, Abe Makoto, Watanabe Akinori

机构信息

Department of Cardiology, Fujieda Municipal General Hospital, Japan.

出版信息

Intern Med. 2021 Mar 22. doi: 10.2169/internalmedicine.7052-21.

Abstract

Painful left bundle branch block (LBBB) syndrome is a rare disease that presents as simultaneous chest pain and transient LBBB without myocardial ischemia. We diagnosed a 72-year-old Japanese man with painful LBBB syndrome complicated by iron-overload cardiomyopathy. Phlebotomy was initially performed to improve myocardial iron deposition and conductive disturbance. Ironically, his chest pain was fully improved by the completion of incessant LBBB and walk-through phenomenon. However, this case demonstrates a clinically significant therapeutic strategy for cardiomyopathy-induced painful LBBB syndrome. Due to the lack of treatment guidelines, individualized treatment is required for each case of painful LBBB.

摘要

疼痛性左束支传导阻滞(LBBB)综合征是一种罕见疾病,表现为同时出现胸痛和短暂性LBBB且无心肌缺血。我们诊断出一名72岁的日本男性患有疼痛性LBBB综合征,并伴有铁过载性心肌病。最初进行了静脉放血以改善心肌铁沉积和传导障碍。具有讽刺意味的是,在持续性LBBB和贯穿现象完成后,他的胸痛完全缓解。然而,该病例展示了一种针对心肌病所致疼痛性LBBB综合征具有临床意义的治疗策略。由于缺乏治疗指南,对于每例疼痛性LBBB都需要个体化治疗。

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