Giannini S, Ceccarelli F, Granata C, Capelli T, Merlini L
Department of Orthopaedic Surgery, University of Bologna, Italy.
Neuropediatrics. 1988 May;19(2):105-8. doi: 10.1055/s-2008-1052411.
The rigid spine syndrome is a condition characterized by a mild axial and proximal myopathy in which the fibrous shortening of spinal extensor muscles causes a marked limitation in flexion of the spine. This 10-year-old boy with rigid spine syndrome showed a progressive limitation in flexion of the cervical spine with fixed hyperextension of the neck. To look forward he had to bend forward his trunk flexing hips and knees. An X-ray study demonstrated a progressive limitation in flexion but also in extension of the cervical spine. A particular radiologic aspect named "Alligator sign" was demonstrated. The hyperextension of the neck was corrected surgically by opening the interspinous spaces from C2 to C7 through a capsulotomy. The correction was stabilized with bone grafts fixed to the spinous processes. This boy with the straightened cervical spine was then able to look forward without any compensatory posture.
僵硬脊柱综合征是一种以轻度轴性和近端肌病为特征的疾病，其中脊柱伸肌的纤维性缩短导致脊柱前屈明显受限。这名患有僵硬脊柱综合征的10岁男孩表现出颈椎前屈逐渐受限，颈部固定性过伸。为了向前看，他不得不向前弯曲躯干，屈曲臀部和膝盖。X线检查显示颈椎前屈逐渐受限，同时后伸也受限。显示出一种特殊的放射学表现，称为“鳄鱼征”。通过经关节囊切开术打开C2至C7的棘突间隙，手术矫正颈部过伸。用固定在棘突上的骨移植稳定矫正效果。这名颈椎伸直的男孩此后能够向前看而无需任何代偿姿势。
