Manzoni G A, Rossi M V, Giacomoni M A, Volpi M L
Divisione di Chirurgia Infantile, Ospedale Niguarda Ca' Granda, Milano, Italia.
Pediatr Med Chir. 1988 Jan-Feb;10(1):93-7.
Renal ectopy is a rare congenital malformation related to an abnormal migration of the kidney from the sacral to the lumbar region. Three possibilities are present: absent migration (pelvic ectopia), excessive (intrathoracic ectopia) or to the opposite side (crossed ectopia). During the last 10 years in the Department of Pediatric Surgery of the Niguarda Hospital 13 cases of renal ectopy have been observed. Five patients had a crossed ectopy (4 with fusion) and eight had a simple ectopy (1 intrathoracic, 7 pelvic). Female were more affected than males (9 cases) and the right side was involved in 8 cases, the left in 4 cases and both kidneys in 1 case. Associated anomalies were present in 7 patients: 6 cases with exclusively genito-urinary malformations while 1 patient only was polimalformed (cloacal exstrophy, MMC, bilateral TEV). Correct diagnosis was obtained during urologic screening in 5 cases (1 suspected antenatally), while in 7 cases was related to the associated symptoms (UTI, hematuria, abdominal pain). Seven patients were surgically treated for the associated urologic abnormalities while in the remaining six cases no treatment was required.
肾异位是一种罕见的先天性畸形，与肾脏从骶骨区域向腰椎区域的异常迁移有关。存在三种可能性：迁移缺失（盆腔异位）、过度迁移（胸腔内异位）或迁移至对侧（交叉异位）。在过去10年里，尼瓜尔达医院小儿外科观察到13例肾异位病例。5例为交叉异位（4例伴有融合），8例为单纯异位（1例胸腔内异位，7例盆腔异位）。女性比男性更易受累（9例），右侧受累8例，左侧受累4例，双侧肾脏受累1例。7例患者存在相关畸形：6例仅有泌尿生殖系统畸形，而1例患者存在多种畸形（泄殖腔外翻、脊髓脊膜膨出、双侧马蹄内翻足）。5例患者在泌尿外科筛查时得到正确诊断（1例产前疑似），而7例与相关症状有关（尿路感染、血尿、腹痛）。7例患者因相关泌尿系统异常接受了手术治疗，其余6例无需治疗。
