Yokoyama Kenji, Yoshizaki Tomoya, Tasaki Dai
Department of Cardiovascular Surgery, Musashino Red Cross Hospital, 1-26-1 Kyonancho, Musashino-city, Tokyo, 180-8610, Japan.
Surg Case Rep. 2021 Mar 23;7(1):75. doi: 10.1186/s40792-021-01158-y.
Primary cardiac schwannoma in the left atrium and schwannomatosis are rare diseases.
We report the case of a 46-year-old asymptomatic man who had tumor resection for parapharyngeal schwannoma at another institute 1 year ago. He was presented to our hospital for further evaluation of an abnormal cardiac shadow that was found incidentally. Computed tomography and transesophageal echocardiography revealed a cardiac tumor originating from the posterior wall of the left atrium, an atrial septal defect, and two other mediastinal tumors. The cardiac mass was completely excised with normal margins of the surrounding atrial wall. The post-resection defect and atrial septal defect were repaired using bovine pericardium. Pathological findings were compatible with benign schwannoma, and a diagnosis of schwannomatosis was made based on his medical history.
Primary cardiac schwannoma is an exceedingly rare tumor, and the incidence in schwannomatosis has not been reported in the literature.
原发性左心房神经鞘瘤和神经鞘瘤病是罕见疾病。
我们报告一例46岁无症状男性病例，该患者1年前在另一机构因咽旁神经鞘瘤接受了肿瘤切除术。他因偶然发现的心脏阴影异常前来我院进一步评估。计算机断层扫描和经食管超声心动图显示，心脏肿瘤起源于左心房后壁，伴有房间隔缺损以及另外两个纵隔肿瘤。心脏肿块被完整切除，周围心房壁边缘正常。切除术后的缺损和房间隔缺损采用牛心包进行修复。病理结果符合良性神经鞘瘤，根据其病史诊断为神经鞘瘤病。
原发性心脏神经鞘瘤是一种极其罕见的肿瘤，文献中尚未报道神经鞘瘤病中的发病率。
