Department of Internal Medicine, East Carolina University, Greenville, NC, 27834, USA.
Vidant Heart and vascular Care, Vidant Medical Center, Greenville, NC, 27834, USA.
BMC Cardiovasc Disord. 2021 Mar 25;21(1):153. doi: 10.1186/s12872-020-01750-4.
We report a rare case of a patient who presented with chest pain and was found to have a constellation of rare cardiac anomalies.
A 67-year-old patient with no past medical history presented with chest pain. He had mild troponin elevation, but no ischemic changes on ECG. He underwent a CT coronary angiogram for further evaluation. He was found to have a type 0 bicuspid aortic valve, large left sinus of Valsalva aneurysm and type R-III single coronary artery. These findings were confirmed with transesophageal echocardiogram and coronary angiogram. He underwent a successful repair of his aortic root aneurysm with a synthetic patch.
The combination of type R-III single coronary artery, bicuspid aortic valve, and left sinus of Valsalva aneurysm congenital anomalies in one individual is extremely rare and marks our case unique. Given the size of his Sinus of Valsalva aneurysm, the patient underwent surgical repair of his aneurysm and was asymptomatic when seen in follow-up.
我们报告了一例罕见的胸痛患者,该患者存在一系列罕见的心脏畸形。
一位 67 岁的患者,无既往病史,因胸痛就诊。他的肌钙蛋白轻度升高,但心电图无缺血改变。他行 CT 冠状动脉造影以进一步评估。发现他有 0 型二叶式主动脉瓣、大的左冠状动脉窦瘤和 R-III 型单冠状动脉。经食管超声心动图和冠状动脉造影证实了这些发现。他成功地用合成补片修复了主动脉根部瘤。
在一个个体中同时存在 R-III 型单冠状动脉、二叶式主动脉瓣和左冠状动脉窦瘤先天性畸形极为罕见,这使我们的病例具有独特性。鉴于他的冠状动脉窦瘤的大小,患者接受了手术修复,随访时无症状。