Evans Emily, McDonald Mandy, Adamson Dawn L, Khan Jamal Nasir
University Hospital Coventry & Warwickshire, Clifford Bridge Road, Coventry CV2 2DX, UK.
Eur Heart J Case Rep. 2021 Mar 22;5(3):ytab088. doi: 10.1093/ehjcr/ytab088. eCollection 2021 Mar.
Left ventricular non-compaction (LVNC) cardiomyopathy is a persistence of abnormal foetal myocardium and is a rare cause of cardiomyopathy in the peripartum period. Unlike other causes of peripartum cardiomyopathy which typically improve, LVNC has significant long-term personal and family implications and needs lifelong follow-up.
We describe a unique case of a 30-year-old woman who developed cardiomyopathy in the peripartum period which was revealed on cardiovascular magnetic resonance imaging to be due to occult LVNC. Our patient also had Ebstein's anomaly, which is a known LVNC association.
Cardiomyopathy in the peripartum period can be a decompensation of previously asymptomatic subclinical cardiomyopathy. It is important to assess for LVNC in patients presenting with this. Cardiovascular magnetic resonance imaging is the gold-standard imaging modality and allows accurate diagnosis of LVNC, associated structural complications and rare associations such as Ebstein's anomaly. Left ventricular non-compaction is irreversible and has implications for patients and their family members.
左心室心肌致密化不全（LVNC）心肌病是胎儿期异常心肌的持续存在，是围产期心肌病的罕见病因。与其他通常会改善的围产期心肌病病因不同，LVNC具有重大的长期个人和家庭影响，需要终身随访。
我们描述了一例独特的病例，一名30岁女性在围产期发生心肌病，心血管磁共振成像显示其病因是隐匿性LVNC。我们的患者还患有埃布斯坦畸形，这是一种已知与LVNC相关的疾病。
围产期心肌病可能是先前无症状的亚临床心肌病的失代偿。对出现这种情况的患者评估LVNC很重要。心血管磁共振成像是金标准成像方式，可准确诊断LVNC、相关的结构并发症以及诸如埃布斯坦畸形等罕见关联。左心室心肌致密化不全是不可逆的，对患者及其家庭成员都有影响。
