Paediatric Dentistry, Pakistan Institute of Medical Sciences, Islamabad, Pakistan.
University College of Dentistry, Lahore, Pakistan.
J Ayub Med Coll Abbottabad. 2021 Jan-Mar;33(1):159-161.
Congenital maxillomandibular syngnathia is characterized by fusion of jaws. Depending on the severity, it has a wide range of clinical presentations. It can be complete /incomplete and may be unilateral or bilateral. Primary concern in such patients is maintenance of airway and feeding difficulties. Therefore, early recognition and management is important to reduce nutritional, feeding, airway difficulties and growth-related problems in such new-borns. This case report presents a case of syngnathia in a 4-day infant with bilateral fusion of maxilla and mandible, leaving a small anterior portion. Early intervention was planned and the fusion was released to facilitate feeding. Good mouth opening was seen on 1week follow-up.
先天性下颌上颌联合畸形的特征是颌骨融合。根据严重程度，其临床表现广泛。它可以是完全的/不完全的，可能是单侧的或双侧的。此类患者的主要关注点是保持气道通畅和解决喂养困难。因此，早期识别和管理对于减少此类新生儿的营养、喂养、气道困难和生长相关问题非常重要。本病例报告介绍了一例 4 天大的婴儿双侧上颌和下颌融合，仅留下一小部分前部分的联合畸形。计划进行早期干预，并释放融合以促进喂养。在 1 周随访时，观察到良好的张口度。
