Department of Pediatrics, Emory University School of Medicine, Atlanta, GA 30322, USA.
Center for CF & Airways Disease Research, Children's Healthcare of Atlanta, Atlanta, GA 30322, USA.
Int J Mol Sci. 2021 Mar 3;22(5):2530. doi: 10.3390/ijms22052530.
Cystic fibrosis (CF) lung disease is dominated by the recruitment of myeloid cells (neutrophils and monocytes) from the blood which fail to clear the lung of colonizing microbes. In prior in vitro studies, we showed that blood neutrophils migrated through the well-differentiated lung epithelium into the CF airway fluid supernatant (ASN) mimic the dysfunction of CF airway neutrophils in vivo, including decreased bactericidal activity despite an increased metabolism. Here, we hypothesized that, in a similar manner to neutrophils, blood monocytes undergo significant adaptations upon recruitment to CFASN. To test this hypothesis, primary human blood monocytes were transmigrated in our in vitro model into the ASN from healthy control (HC) or CF subjects to mimic in vivo recruitment to normal or CF airways, respectively. Surface phenotype, metabolic and bacterial killing activities, and transcriptomic profile by RNA sequencing were quantified post-transmigration. Unlike neutrophils, monocytes were not metabolically activated, nor did they show broad differences in activation and scavenger receptor expression upon recruitment to the CFASN compared to HCASN. However, monocytes recruited to CFASN showed decreased bactericidal activity. RNASeq analysis showed strong effects of transmigration on monocyte RNA profile, with differences between CFASN and HCASN conditions, notably in immune signaling, including lower expression in the former of the antimicrobial factor ISG15, defensin-like chemokine CXCL11, and nitric oxide-producing enzyme NOS3. While monocytes undergo qualitatively different adaptations from those seen in neutrophils upon recruitment to the CF airway microenvironment, their bactericidal activity is also dysregulated, which could explain why they also fail to protect CF airways from infection.
囊性纤维化(CF)肺部疾病的特征是骨髓细胞(中性粒细胞和单核细胞)从血液中募集,但未能清除定植微生物。在之前的体外研究中,我们表明,血液中性粒细胞穿过分化良好的肺上皮细胞进入 CF 气道液上清液(ASN),模拟了 CF 气道中性粒细胞的功能障碍,包括杀菌活性降低,尽管代谢增加。在这里,我们假设,类似于中性粒细胞,血液单核细胞在招募到 CFASN 时会发生重大适应。为了验证这一假设,我们在体外模型中使原代人血液单核细胞穿过 CF 患者或健康对照者的 ASN,分别模拟体内对正常或 CF 气道的招募。在迁移后定量测量表面表型、代谢和细菌杀伤活性以及通过 RNA 测序的转录组谱。与中性粒细胞不同,单核细胞没有被代谢激活,也没有在招募到 CFASN 时与 HCASN 相比表现出广泛的激活和清道夫受体表达差异。然而,招募到 CFASN 的单核细胞的杀菌活性降低。RNAseq 分析显示,迁移对单核细胞 RNA 谱有强烈影响,CFASN 和 HCASN 条件之间存在差异,特别是在免疫信号中,前者抗菌因子 ISG15、防御素样趋化因子 CXCL11 和产生一氧化氮的酶 NOS3 的表达降低。虽然单核细胞在招募到 CF 气道微环境时经历了与中性粒细胞不同的适应,但它们的杀菌活性也失调,这可以解释为什么它们也不能保护 CF 气道免受感染。