Physician in the Angiology and Vascular Surgery Department, San Carlos Clinical Hospital, Madrid.
Physician in the Angiology and Vascular Surgery Department, San Carlos Clinical Hospital, Madrid.
Ann Vasc Surg. 2021 Aug;75:532.e9-532.e13. doi: 10.1016/j.avsg.2021.03.025. Epub 2021 Apr 6.
Aortic dissection is exceptional in children. When they are affected, many clinical conditions as Marfan syndrome or Ehlers-Danlos syndrome are usually involved, but up to 22% have no associated background. Its high morbidity and low incidence in this age group require a high level of suspicion in children without predisposing factors when the presentation is atypical, to avoid the severe consequences of the delay of their diagnosis. In this article we describe the dissection and aortic rupture in a 12-year-old child without relevant medical history, and the open repair that was performed as treatment.
主动脉夹层在儿童中较为罕见。当儿童受到影响时，通常涉及多种临床情况，如马凡综合征或埃勒斯-当洛斯综合征，但高达 22%的儿童没有相关背景。由于该年龄段的发病率高，且主动脉夹层在该年龄段的发病率较低，因此当临床表现不典型且无诱发因素时，对于没有潜在因素的儿童，需要高度怀疑该病，以避免因诊断延迟而导致严重后果。本文描述了一例 12 岁儿童无相关病史的主动脉夹层和主动脉破裂，并对其进行了开放性修复治疗。
