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新生儿扩张型心肌病行 Norwood 手术合并部分左心室切除术。

Norwood Operation With Partial Left Ventriculectomy for Neonatal Dilated Cardiomyopathy.

机构信息

Department of Cardiothoracic Surgery, University of Louisville, Norton Children's Hospital, Louisville, Kentucky.

Department of Pediatrics, University of Louisville, Norton Children's Hospital, Louisville, Kentucky.

出版信息

Ann Thorac Surg. 2022 Feb;113(2):e137-e139. doi: 10.1016/j.athoracsur.2021.04.020. Epub 2021 Apr 20.

Abstract

The combination of severe fetal mitral regurgitation diagnosed in utero, aortic stenosis, left ventricular dilatation, and dysfunction is associated with extremely poor prognosis. We report a neonate who underwent Norwood operation and left ventricular exclusion using partial left ventriculotomy and Alfieri mitral valve stitch. Left ventricular exclusion eliminated right ventricular compression and allowed survival and progression to subsequent second-stage palliation.

摘要

胎儿二尖瓣重度反流、主动脉瓣狭窄、左心室扩张和功能障碍的联合诊断与极差的预后相关。我们报告了一例新生儿,该新生儿接受了 Norwood 手术和左心室排除术,采用了部分左心室切开术和 Alfieri 二尖瓣缝合术。左心室排除术消除了右心室的压迫,使患儿得以存活并进行后续的二期姑息治疗。

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