Department of Otorhinolaryngology, Head and Neck Surgery, Meyer Children's Hospital, Florence, Italy.
Pathology Unit, Meyer Children's Hospital, Florence, Italy.
J Int Adv Otol. 2021 Mar;17(2):150-155. doi: 10.5152/JIAO.2021.8491.
A rare pediatric case report of middle ear neuroendocrine tumor and review of the pediatric cases reported in the literature. A 16-year-old female showed a lesion occupying the posterosuperior part of the medial third of the right external auditory canal confirmed by computed tomography scan, without clear evidence of bone erosion. The patient underwent canal wall tympanoplasty in 1 stage. No residual pathology was present after 1 month, 3-6 months, and after 1 year. There are few known pediatric cases of this disease, there is no statistically significant data for this population regarding the risk of recurrence or metastasis. Middle ear neuroendocrine tumors are rare above all in children. They are slow aggressive tumors but they can recur and rarely give local metástasis. Only 4 pediatric cases have been published. We have completely removed the tumor in our patient, using a conservative surgical treatment in a single stage.
罕见儿童中耳神经内分泌肿瘤病例报告及文献中报道的儿科病例回顾。一名 16 岁女性的 CT 扫描显示病变占据了右侧外耳道中三分之一的后上方，没有明显的骨侵蚀证据。患者接受了 1 期鼓室成形术。1 个月、3-6 个月和 1 年后均无残留病理学表现。这种疾病在儿童中很少见，针对该人群的复发或转移风险，尚无统计学意义的数据。中耳神经内分泌肿瘤在儿童中尤为罕见。它们是缓慢侵袭性肿瘤，但可能复发，很少发生局部转移。仅有 4 例儿科病例已发表。我们在患者中完全切除了肿瘤，采用了单阶段的保守手术治疗。
