Division of Cardiology, The Cardiac Center at The Children's Hospital of Philadelphia, PA, USA.
Division of Nephrology, The Children's Hospital of Philadelphia, PA, USA.
World J Pediatr Congenit Heart Surg. 2021 Sep;12(5):673-675. doi: 10.1177/2150135120978959. Epub 2021 Apr 25.
The hemodynamic profile of the Fontan circulation presents challenges that raise questions about candidacy for organ transplantation. We report a case of a 24-year-old male with double-inlet right ventricle and aortic atresia, who suffered bilateral renal cortical necrosis due to neonatal cardiovascular shock, received a live-donor kidney transplant from his mother at age 17, and has diminished yet stable renal function seven years posttransplant.
法洛四联症循环的血液动力学特征带来了一些挑战，这些挑战引发了有关其是否适合接受器官移植的问题。我们报告了一例 24 岁男性的病例，该患者患有双入口右心室和主动脉瓣闭锁，因新生儿心血管休克导致双侧肾皮质坏死，在 17 岁时接受了来自母亲的活体供肾移植，并且在移植后 7 年，肾功能虽然有所下降但仍然稳定。
