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法洛四联症经跨瓣环补片修补术后晚期出现的原发性肺动脉瓣关闭不全。

Native Pulmonary Valve Restoration Late Following Transannular Patch Repair of Tetralogy of Fallot.

机构信息

Cardiac Services, 4593Alder Hey Children's NHS Foundation Trust, Eaton Road, Liverpool, United Kingdom.

Faculty of Health, Liverpool John Moores University, Kingsway House, Liverpool, United Kingdom.

出版信息

World J Pediatr Congenit Heart Surg. 2021 Sep;12(5):677-679. doi: 10.1177/2150135120981056. Epub 2021 May 4.

DOI:10.1177/2150135120981056
PMID:33947283
Abstract

We present a surgical case of native pulmonary valve (PV) restoration in a 16-year-old boy with a previous history of transannular patch repair of tetralogy of Fallot in infancy. The PV was restored by approximation of split anterior commissure in the presence of developed and pliable leaflets well preserved after initial surgery. Postoperative echocardiogram showed a competent valve with peak velocity of 2.8 m/s. At six-week follow-up, the patient remained well, and echocardiogram demonstrated a competent PV with decreased velocity of 2.1 m/s across it. We encourage a mindful preservation of PV leaflets whenever it is possible at time of initial repair to implement this relatively easy operation to restore PV function later in life.

摘要

我们报告了 1 例先心患儿的手术病例,该患儿曾在婴儿期因法洛四联症接受过经肺动脉瓣环补片的矫正手术。该患儿此次接受了肺动脉瓣切开后前交界对位术,保留了初始手术后发育良好且有弹性的瓣叶,从而实现了肺动脉瓣的修复。术后超声心动图显示,瓣膜功能良好,峰值流速为 2.8m/s。6 周后随访时,患者情况良好,超声心动图显示,跨瓣口流速为 2.1m/s,瓣膜功能良好。我们鼓励在初次修复时尽可能保留肺动脉瓣叶,以便在以后的生活中实施相对简单的手术来恢复肺动脉瓣功能。

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World J Pediatr Congenit Heart Surg. 2021 Sep;12(5):677-679. doi: 10.1177/2150135120981056. Epub 2021 May 4.
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