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单尖瓣单叶主动脉瓣、升主动脉瘤和牛型弓:一例罕见病例报告。

Unicommissural Unicuspid Aortic Valve, Ascending Aortic Aneurysm, and Bovine Arch: A Rare Case Report.

机构信息

Banner University Medical Center, Phoenix, AZ, USA.

Phoenix Children's Hospital, Phoenix, AZ, USA.

出版信息

World J Pediatr Congenit Heart Surg. 2021 Nov;12(6):787-790. doi: 10.1177/2150135120965201. Epub 2021 May 6.

DOI:10.1177/2150135120965201
PMID:33956546
Abstract

A 24-year-old man presented with rapidly progressive dyspnea due to mixed aortic stenosis and insufficiency. Unicommissural unicuspid aortic valve, ascending aortic aneurysm, and a bovine arch were identified on computed tomography angiography. Uncomplicated surgical mechanical valve replacement and ascending aortic graft placement improved his symptoms. Aortopathy is common in unicuspid valve patients.

摘要

一位 24 岁男性因混合性主动脉瓣狭窄和关闭不全导致进行性呼吸困难。计算机断层血管造影术发现单孔单瓣主动脉瓣、升主动脉瘤和牛型弓。单纯手术机械瓣置换和升主动脉移植物置入改善了他的症状。单瓣病变患者常合并主动脉病变。

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