Department of Pediatrics, Peking University People's Hospital, Beijing, P.R. China.
Department of Pediatrics, Peking University First Hospital, Beijing, P.R. China.
Pediatr Neurol. 2021 Jul;120:27-32. doi: 10.1016/j.pediatrneurol.2021.04.001. Epub 2021 Apr 7.
Autoimmune encephalitis (AE) is an increasingly recognized inflammatory disorder of the central nervous system and is most often characterized by antibodies against intracellular and neuronal surface antigens. AE is a devastating disease that may result in developmental delay or regression in children. However, the pathogenesis of AE is not clear, and immune system disorders after infection likely play an important role in AE. Many studies have reported that patients with herpes simplex virus encephalitis develop anti-N-methyl-d-aspartate receptor encephalitis after antiviral treatment. It is critical to recognize pediatric AE early and to distinguish it from infectious forms because AE is treatable and responsive to immunotherapies. In this review, we discuss the clinical features of pediatric AE and focus on the relationship between AE and postinfection status. In addition, we review the probable mechanisms underlying infection-triggered AE, which include molecular mimicry, bystander activation, epitope spreading, immune system disorder, and genetic susceptibility.
自身免疫性脑炎(AE)是一种中枢神经系统炎症性疾病,越来越受到重视,其特征通常为针对细胞内和神经元表面抗原的抗体。AE 是一种破坏性疾病,可能导致儿童发育迟缓或倒退。然而,AE 的发病机制尚不清楚,感染后的免疫系统紊乱可能在 AE 中起重要作用。许多研究报告称,单纯疱疹病毒脑炎患者在抗病毒治疗后会发生抗 N-甲基-D-天冬氨酸受体脑炎。早期识别儿科 AE 并将其与感染性疾病区分开来非常重要,因为 AE 是可治疗的,对免疫疗法有反应。在这篇综述中,我们讨论了儿科 AE 的临床特征,并重点介绍了 AE 与感染后状态的关系。此外,我们还回顾了感染引发 AE 的可能机制,包括分子模拟、旁观者激活、表位扩展、免疫系统紊乱和遗传易感性。