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马蹄肾合并肾肿瘤与腔静脉紧密粘连的部分开放性肿瘤切除术:一例报告

Partial open tumorectomy for a renal tumor in a horseshoe kidney with a close contact with the vena cava: A case report.

作者信息

Saadi Mohamed Hafedh, Chakroun Marouene, Saadi Ahmed, Derouiche Amine, Ayed Haroun, Chebil Mohamed

机构信息

Urology Department, Charles Nicolle Hospital, Tunis, Tunisia.

Urology Department, Charles Nicolle Hospital, Tunis, Tunisia.

出版信息

Int J Surg Case Rep. 2021 May;82:105923. doi: 10.1016/j.ijscr.2021.105923. Epub 2021 Apr 27.

DOI:10.1016/j.ijscr.2021.105923
PMID:33965759
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC8114110/
Abstract

INTRODUCTION AND IMPORTANCE

Horseshoe kidney has unique anatomical features, such as a complex blood supply. We report a patient with renal tumor in a horseshoe kidney in close contact with the vena cava, who underwent open tumorectomy.

CASE PRESENTATION

A 72-year-old woman was referred to our hospital with a 4-cm enhancing mid-pole mass in the right moiety of a horseshoe kidney. Open tumorectomy was performed with parenchymal clamping. The warm ischemia time was 18 min. Pathologic examination confirmed a diagnosis of pT1a clear cell renal cell carcinoma with negative surgical margins. At 3 months postoperatively, computed tomography showed no local recurrence or metastasis and renal function was intact.

CLINICAL DISCUSSION

Horseshoe kidney is a rare congenital abnormality. Renal cell carcinoma is the most frequent tumor in adults having this anomaly and treatment in localised tumors if usually tumorectomy. Surgery may be challenging in some cases because of its difficulty.

CONCLUSION

Open surgery remains the standard treatment for horseshoe kidney tumors because of anatomic complexity and especially in cases where the tumor is difficult to extirpate.

摘要

引言与重要性

马蹄肾具有独特的解剖学特征,如复杂的血液供应。我们报告一例马蹄肾合并肾肿瘤且与腔静脉紧密相邻的患者,该患者接受了开放性肿瘤切除术。

病例介绍

一名72岁女性因马蹄肾右侧部分中极有一个4厘米的强化肿块被转诊至我院。采用实质钳夹进行开放性肿瘤切除术。热缺血时间为18分钟。病理检查确诊为pT1a期透明细胞肾细胞癌,手术切缘阴性。术后3个月,计算机断层扫描显示无局部复发或转移,肾功能完好。

临床讨论

马蹄肾是一种罕见的先天性异常。肾细胞癌是患有这种异常的成年人中最常见的肿瘤,对于局限性肿瘤通常采用肿瘤切除术进行治疗。由于手术难度,某些情况下手术可能具有挑战性。

结论

由于解剖结构复杂,尤其是在肿瘤难以切除的情况下,开放性手术仍然是马蹄肾肿瘤的标准治疗方法。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4d5e/8114110/485c57acbd7e/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4d5e/8114110/7b6667695041/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4d5e/8114110/629e71891cbd/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4d5e/8114110/485c57acbd7e/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4d5e/8114110/7b6667695041/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4d5e/8114110/629e71891cbd/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4d5e/8114110/485c57acbd7e/gr3.jpg

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