Yadav Manisha, Hayashi Tokumasa, Krisna Ratih, Nutthachote Pattiya, Sawada Yogo, Tokiwa Shino, Cortes Auran Rosanne, Nomura Masayoshi
Urogynecology Center, Kameda Medical Center, Kamogawa, Chiba, Japan.
Case Rep Womens Health. 2021 Apr 17;30:e00313. doi: 10.1016/j.crwh.2021.e00313. eCollection 2021 Apr.
Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome is a rare congenital anomaly that results in Müllerian agenesis that affects the uterus and upper two-thirds of the vagina. Sigmoid vaginoplasty is a surgical treatment option; however, vaginal prolapse may result as a complication of the sigmoid neovagina. There are no standards for treatment due to the rarity of this condition. We present the case of a 59-year-old woman with a history of sigmoid vaginoplasty who underwent laparoscopic sacrocolpopexy (LSC) for grade IV sigmoid stump prolapse. The patient had a successful outcome and no evidence of recurrent prolapse. This clinical case reveals the feasibility of LSC as a surgical treatment for sigmoid stump prolapses in patients with MRKH syndrome.
迈耶-罗基坦斯基-库斯特-豪泽(MRKH)综合征是一种罕见的先天性异常,可导致苗勒管发育不全,影响子宫和阴道上三分之二。乙状结肠阴道成形术是一种手术治疗选择;然而,乙状结肠新阴道可能会出现阴道脱垂并发症。由于这种疾病罕见,目前尚无治疗标准。我们报告一例59岁有乙状结肠阴道成形术史的女性患者,因IV级乙状结肠残端脱垂接受腹腔镜骶骨阴道固定术(LSC)。患者手术成功,无复发脱垂迹象。该临床病例揭示了LSC作为MRKH综合征患者乙状结肠残端脱垂手术治疗方法的可行性。