Weisbrod Luke J, Liu Collin, Surdell Daniel
Neurological Surgery, University of Nebraska Medical Center, Omaha, USA.
Neurosurgery, University of Nebraska Medical Center, Omaha, USA.
Cureus. 2021 Apr 13;13(4):e14460. doi: 10.7759/cureus.14460.
Ventriculus terminalis (VT) is a cystic embryological remnant within the conus medullaris that normally regresses after birth. In rare cases, it may persist into adulthood and give rise to neurologic symptoms. The pathogenesis remains unclear but is thought to be related to failed embryonic regression with other proposed possible etiologies including vascular disturbances. We present an intriguing case of a slow-growing VT in a woman with progressive neurologic symptoms who experiences symptomatic relief following thoracic laminectomy and fenestration. Our case is the first to present a unique association with polyarteritis nodosa and only the third to report a case of documented enlargement of the VT over time successfully treated with surgical fenestration.
终室（VT）是脊髓圆锥内的一个囊性胚胎残留物，通常在出生后消退。在罕见情况下，它可能持续至成年并引发神经症状。其发病机制尚不清楚，但被认为与胚胎退化失败有关，其他可能的病因包括血管紊乱。我们报告了一例有趣的病例，一名患有进行性神经症状的女性，其终室生长缓慢，在接受胸椎椎板切除术和开窗术后症状缓解。我们的病例是首例与结节性多动脉炎有独特关联的病例，也是第三例报告经手术开窗成功治疗后终室随时间记录到增大的病例。
