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尺神经原发性霍奇金淋巴瘤:首例病例报告并文献复习

Primary Hodgkin lymphoma of the ulnar nerve: the first case report with review of the literature.

作者信息

Derqaoui Sabrine, Zouaidia Fouad, Jahid Ahmed, Bernoussi Zakia, Znati Kaoutar

机构信息

Department of Pathology, Ibn Sina Teaching Hospital, Abderrahim Bouabid Avenue, Rabat 12000, Morocco.

出版信息

J Surg Case Rep. 2021 May 20;2021(5):rjab185. doi: 10.1093/jscr/rjab185. eCollection 2021 May.

DOI:10.1093/jscr/rjab185
PMID:34040754
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC8136864/
Abstract

Hodgkin lymphoma is a lymphoid malignancy characterized by minority population of neoplastic cells (Reed-Sternberg cells and its variants) within a reactive inflammatory background. It encompasses two entities: classical HL (∼95% of cases) and nodular lymphocyte predominant HL (∼5% of cases). Primary lymphoma of peripheral nerves (PLPN) represent a very rare condition, since only 19 cases have been reported in the English literature to date, all of which are of a non-HL phenotype. A 20-year-old female presented an intramural mass of the ulnar nerve. Histological analysis revealed a Classical Hodgkin lymphoma. Further investigations failed to reveal nodal or extranodal involvement. PLPN is a very rare entity. There is a need for further understanding of this unusual lymphoma presentation.

摘要

霍奇金淋巴瘤是一种淋巴系统恶性肿瘤,其特征是在反应性炎症背景中存在少数肿瘤细胞(里德-施特恩贝格细胞及其变体)。它包括两个类型:经典型霍奇金淋巴瘤(约占病例的95%)和结节性淋巴细胞为主型霍奇金淋巴瘤(约占病例的5%)。周围神经原发性淋巴瘤(PLPN)是一种非常罕见的疾病,因为迄今为止英文文献中仅报道了19例,所有这些病例均为非霍奇金淋巴瘤表型。一名20岁女性出现尺神经壁内肿块。组织学分析显示为经典型霍奇金淋巴瘤。进一步检查未发现淋巴结或结外受累。PLPN是一种非常罕见的疾病。有必要进一步了解这种不寻常的淋巴瘤表现形式。

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本文引用的文献

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Hodgkin lymphoma: A 2020 update on diagnosis, risk-stratification, and management.霍奇金淋巴瘤:2020 年诊断、风险分层和治疗的更新。
Am J Hematol. 2020 Aug;95(8):978-989. doi: 10.1002/ajh.25856. Epub 2020 Jun 8.
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Primary B lymphoma tumor of the ulnar nerve. Case report.尺神经原发性B淋巴瘤。病例报告。
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Hodgkin lymphoma: pathology, pathogenesis, and a plethora of potential prognostic predictors.霍奇金淋巴瘤:病理学、发病机制及大量潜在的预后预测指标。
Adv Anat Pathol. 2014 Jan;21(1):12-25. doi: 10.1097/PAP.0000000000000002.
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Pathobiology of hodgkin lymphoma.霍奇金淋巴瘤的病理生物学
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Hodgkin's Lymphoma: A Review of Neurologic Complications.霍奇金淋巴瘤:神经系统并发症综述
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