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胎儿二尖瓣口开放、主动脉闭锁及严重左心扩大。

Fetal Unguarded Mitral Valve Orifice, Aortic Atresia, and Severe Left Heart Enlargement.

作者信息

Howley Lisa W, Strasburger Janette, Maleszewski Joseph J, Snowise Saul, Lund Amy, Schneider Andrew, MacIver Robroy, Edens Erik, Eyerly-Webb Stephanie, Silverman Norman H

机构信息

Division of Cardiology, Department of Pediatrics, The Children's Heart Clinic, Children's Minnesota, Minneapolis, Minnesota, USA.

Midwest Fetal Care Center, Children's Minnesota, Minneapolis, Minnesota, USA.

出版信息

JACC Case Rep. 2021 Feb;3(2):206-211. doi: 10.1016/j.jaccas.2020.11.020. Epub 2021 Jan 13.

DOI:10.1016/j.jaccas.2020.11.020
PMID:34041497
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC8145915/
Abstract

Unguarded mitral valve orifice is a rare disease with only 7 described cases in the literature. We describe the first known case of unguarded mitral valve orifice with normal segmental cardiac anatomy, severe left ventricular dilatation and dysfunction, aortic atresia, and atrial flutter. ().

摘要

无保护二尖瓣口是一种罕见疾病，文献中仅报道过7例。我们描述了首例已知的无保护二尖瓣口病例，其心脏节段解剖结构正常，伴有严重左心室扩张和功能障碍、主动脉闭锁及心房扑动。（）

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f588/8310977/fde4123cb7d3/gr4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f588/8310977/0d043855a2b6/fx1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f588/8310977/be414ab95cc8/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f588/8310977/fd15bb882ef4/gr2ab.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f588/8310977/1f90b10c3f80/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f588/8310977/fde4123cb7d3/gr4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f588/8310977/0d043855a2b6/fx1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f588/8310977/be414ab95cc8/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f588/8310977/fd15bb882ef4/gr2ab.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f588/8310977/1f90b10c3f80/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f588/8310977/fde4123cb7d3/gr4.jpg

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1
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引用本文的文献

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2
Society for Cardiovascular Magnetic Resonance 2022 Cases of SCMR case series.社会心血管磁共振学会 2022 年病例系列案例。
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本文引用的文献

1
Caught-off guard: Unguarded mitral valve orifice in usual atrial arrangement with discordant atrioventricular connections and pulmonary atresia.措手不及：在正常心房排列、房室连接不一致及肺动脉闭锁情况下的无保护二尖瓣口。
Ann Pediatr Cardiol. 2020 Jan-Mar;13(1):84-86. doi: 10.4103/apc.APC_4_19. Epub 2019 Jun 26.
2
Unguarded left atrioventricular orifice: An unusual cause of hypoplastic left ventricle and double-outlet right ventricle with intact ventricular septum.无保护的左房室口：左心室发育不全和室间隔完整的右心室双出口的一种罕见病因。
Ann Pediatr Cardiol. 2019 May-Aug;12(2):153-155. doi: 10.4103/apc.APC_124_18.
3
Fatal cardiac anomaly of unguarded mitral orifice with asplenia syndrome.
伴有无脾综合征的致命性心脏异常——无保护二尖瓣口
J Cardiol Cases. 2016 Sep 28;15(1):6-9. doi: 10.1016/j.jccase.2016.09.001. eCollection 2017 Jan.
4
Unguarded tricuspid orifice---a rare cause of fetal right atrial dilatation with characteristic color doppler sign: Case report with review of literature.
J Clin Ultrasound. 2017 Jul 8;45(6):370-374. doi: 10.1002/jcu.22416. Epub 2016 Oct 18.
5
Unguarded mitral orifice associated with hypoplastic left heart syndrome.
Cardiol Young. 2015 Jun;25(5):1002-5. doi: 10.1017/S1047951114001334. Epub 2014 Jul 24.
6
A potential new constellation of defects: unguarded mitral orifice associated with double-outlet right ventricle {I, D, D} and pulmonary atresia/stenosis.
Int J Cardiol. 2011 May 5;148(3):354-7. doi: 10.1016/j.ijcard.2010.06.004. Epub 2010 Jul 2.
7
Norwood procedure combined with the Starnes procedure.诺伍德手术联合斯塔尼斯手术。
Ann Thorac Surg. 2008 Oct;86(4):1378-80. doi: 10.1016/j.athoracsur.2008.03.010.
8
Unguarded mitral orifice associated with discordant atrioventricular connection, double-outlet right ventricle, and pulmonary atresia.
Pediatr Cardiol. 2003 Sep-Oct;24(5):490-2. doi: 10.1007/s00246-002-0389-8.
9
Unguarded mitral orifice, mirror-imaged atrial arrangement, and discordant atrioventricular connections.
Cardiol Young. 1999 Sep;9(5):478-83. doi: 10.1017/s1047951100005382.