Department of Radiology and Research Institute of Radiology, Asan Medical Center, University of Ulsan College of Medicine, Seoul, Korea.
Korean J Radiol. 2021 Sep;22(9):1441-1450. doi: 10.3348/kjr.2021.0034. Epub 2021 May 20.
Anomalous origin of the coronary artery from the pulmonary artery is a rare and potentially fatal congenital heart defect. Up to 90% of infants with an anomaly involving the left coronary artery die within the first year of life if left untreated. Patients who survive beyond infancy are at risk of sudden cardiac death. Cardiac CT and MRI are increasingly being used for the accurate diagnosis of this anomaly for prompt surgical restoration of the dual coronary artery system. Moreover, life-long imaging surveillance after surgery is necessary for these patients. In this pictorial review, multimodal cardiac imaging findings of this rare and potentially fatal coronary artery anomaly are comprehensively discussed, and representative images are provided to facilitate the understanding of this anomaly.
冠状动脉发自肺动脉异常是一种罕见且可能致命的先天性心脏缺陷。未经治疗，90%以上的左冠状动脉受累婴儿会在 1 年内死亡。在婴儿期后存活的患者有发生心源性猝死的风险。心脏 CT 和 MRI 越来越多地用于准确诊断这种异常，以便及时进行双冠状动脉系统的手术重建。此外，这些患者还需要在手术后进行终身影像学监测。在本影像学综述中，全面讨论了这种罕见且可能致命的冠状动脉异常的多模态心脏成像表现，并提供了有代表性的图像，以帮助理解这种异常。
