上颌窦和胸壁滑膜肉瘤：两个同步罕见部位的特殊关联，病例报告
Synovial sarcoma of the maxillary sinus and chest wall: An exceptional association of two synchronous rare locations, Case report.
作者信息
Sabr Ayoub, Azami Hassani Fatema Ez-Zahrae, Iro Salissou, Slimani Faiçal
机构信息
Oral and Maxillofacial Surgery Department, CHU Ibn Rochd, B.P, 2698, Casablanca, Morocco.
Faculty of Medicine and Pharmacy, Hassan II University of Casablanca, B.P, 5696, Casablanca, Morocco.
出版信息
Ann Med Surg (Lond). 2021 Jun 20;67:102523. doi: 10.1016/j.amsu.2021.102523. eCollection 2021 Jul.
INTRODUCTION
Synovial sarcoma is a malignant tumour of mesenchymal origin with an aggressive character and a rare cervicofacial location. Its management is multidisciplinary in order to improve prognosis and survival.
CASE REPORT
We report the case of two rare and synchronous localizations of monophasic synovial sarcoma of the maxilla and chest wall in a 58-year-old woman, whose management was based on exclusive chemotherapy.
DISCUSSION
The cervicofacial location of synovial sarcoma represents 3% of all locations in the body. Its clinical and radiological manifestations are aspecific. Its diagnosis is based on a combination of histological and genetic arguments. Its therapeutic management depends on the tumour stage and prognostic factors.
CONCLUSION
Early diagnosis of cervicofacial synovial sarcoma allows to avoid a mutilating procedure for the patient and to improve the long-term prognosis by a good control of the tumour.
引言
滑膜肉瘤是一种间叶源性恶性肿瘤，具有侵袭性，且在头颈部较为罕见。其治疗需要多学科协作以改善预后和提高生存率。
病例报告
我们报告了一名58岁女性患者，上颌骨和胸壁出现罕见的单相滑膜肉瘤同步局部病变，其治疗仅采用了化疗。
讨论
滑膜肉瘤在头颈部的发病占全身发病部位的3%。其临床和影像学表现不具特异性。诊断基于组织学和遗传学证据的结合。其治疗方案取决于肿瘤分期和预后因素。
结论
头颈部滑膜肉瘤的早期诊断有助于避免患者接受致残性手术，并通过良好的肿瘤控制改善长期预后。
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