Fuller Corey B, Shannon Claire E, Paley Dror
Department of Orthopaedic Surgery, Loma Linda University, Loma Linda, CA 92354, USA.
Paley Orthopedic & Spine Institute, St. Mary's Hospital, West Palm Beach, FL 33407, USA.
Children (Basel). 2021 Jun 2;8(6):467. doi: 10.3390/children8060467.
Fibular hemimelia (FH) presents with foot and ankle deformity and leg length discrepancy. Many historic reconstructions have resulted in poor outcomes. This report reviews modern classification and reconstruction methods. The Paley SHORDT procedure (SHortening Osteotomy Realignment Distal Tibia) is designed to correct dynamic valgus deformity. The Paley SUPERankle procedure (Systematic Utilitarian Procedure for Extremity Reconstruction) is designed to correct fixed equino-valgus foot deformity. The leg length discrepancy in FH is successfully treated with serial lengthening and epiphysiodesis. Implantable intramedullary lengthening devices have led to all internal lengthenings. Recent advancements in techniques and implants in extramedullary implantable limb lengthening (EMILL) have allowed internal lengthenings in younger and smaller patients, who would traditionally require external fixation. These new internal techniques with lengthenings of up to 5 cm can be repeated more easily and frequently than external fixation, reducing the need to achieve larger single-stage lengthenings (e.g., 8 cm). Modern reconstruction methods with lengthening are able to achieve limb length equalization with a plantigrade-stable foot, resulting in excellent functional result comparable or better than a Syme's amputation with prosthetic fitting.
腓骨半肢畸形(FH)表现为足踝畸形和下肢长度不等。许多既往的重建手术效果不佳。本报告回顾了现代分类和重建方法。帕利氏短缩截骨远端胫骨重新排列术(SHortening Osteotomy Realignment Distal Tibia,SHORDT)旨在纠正动态外翻畸形。帕利氏超级踝关节手术(Systematic Utilitarian Procedure for Extremity Reconstruction,SUPERankle)旨在纠正固定性马蹄外翻足畸形。FH中的下肢长度不等可通过系列延长和骨骺阻滞术成功治疗。可植入髓内延长装置已实现了所有的内置延长。髓外可植入肢体延长术(EMILL)在技术和植入物方面的最新进展使得年龄更小、体型更小的患者也能够进行内置延长,而这些患者传统上需要进行外固定。这些新的内置技术延长可达5厘米,比外固定更容易且更频繁地重复进行,减少了实现更大单阶段延长(如8厘米)的需求。采用延长术的现代重建方法能够实现肢体长度均衡,同时足部呈平足且稳定,功能结果优异,可与Syme截肢并安装假肢相媲美甚至更好。