Laroche C M, Carroll N, Moxham J, Stanley N N, Evans R J, Green M
Brompton Hospital, London.
Thorax. 1988 Jun;43(6):478-9. doi: 10.1136/thx.43.6.478.
Two patients are described with Charcot-Marie-Tooth disease and chronic peripheral neuropathy. Both had dyspnoea, orthopnoea, and evidence of severe diaphragm weakness. Expiratory muscle function was well preserved and abnormalities of gas exchange during sleep were only minor.
描述了两名患有夏科-马里-图思病和慢性周围神经病变的患者。两人均有呼吸困难、端坐呼吸以及严重膈肌无力的证据。呼气肌功能保存良好,睡眠期间气体交换仅有轻微异常。