Lopez J R, Allen P, Alamo L, Ryan J F, Jones D E, Sreter F
Centro de Biofisica y Bioquimica, Instituto Venezolano de Investigaciones Cientificas, Caracas, Venezuela.
Cell Calcium. 1987 Oct;8(5):385-96. doi: 10.1016/0143-4160(87)90013-3.
Malignant hyperthermia (MH) is a pharmacogenetic disorder of skeletal muscle triggered when susceptible subjects are exposed to volatile anesthetic agents and/or depolarizing muscle relaxants. We have used Ca2+ selective microelectrodes to measure in vivo the intracellular free [Ca2+] in skeletal muscle of MH susceptible swine before and after the administration of dantrolene. We have investigated the effectiveness of this muscle relaxant in preventing clinical MH and the relationship between the resting intracellular free [Ca2+] and the probability of inducing the MH syndrome. The resting intracellular free [Ca2+] was 0.41 +/- 0.01 microM (M +/- SEM), which agrees with our previous measurements in susceptible swine. The administration of 0.5, 1, 2, 2.5 and 3 mg/Kg Dantrolene, reduced the intracellular free [Ca2+] to 0.31, 0.21, 0.09, 0.08, 0.08 microM respectively. The 0.5 mg/Kg dose induced a moderate decrease of [Ca2+]i and failed to prevent the MH syndrome after exposure to halothane (2%). The 1 mg/Kg dose produced a further reduction in [Ca2+]i and was sufficient to prevent the clinical syndrome in 2 out of 3 animals. The 2.5 mg/Kg dose was uniformly protective in all animals. These results suggest that the mechanism by which dantrolene protects susceptible animals exposed to triggering agents is by reducing the intracellular free [Ca2+] in skeletal muscle.
恶性高热(MH)是一种骨骼肌的药物遗传疾病,当易感个体接触挥发性麻醉剂和/或去极化肌肉松弛剂时会被触发。我们使用钙离子选择性微电极在体内测量了丹曲林给药前后MH易感猪骨骼肌细胞内的游离钙离子浓度。我们研究了这种肌肉松弛剂预防临床MH的有效性,以及静息细胞内游离钙离子浓度与诱发MH综合征可能性之间的关系。静息细胞内游离钙离子浓度为0.41±0.01微摩尔(平均值±标准误),这与我们之前对易感猪的测量结果一致。给予0.5、1、2、2.5和3毫克/千克的丹曲林后,细胞内游离钙离子浓度分别降至0.31、0.21、0.09、0.08、0.08微摩尔。0.5毫克/千克的剂量使钙离子浓度中度降低,在接触氟烷(2%)后未能预防MH综合征。1毫克/千克的剂量使钙离子浓度进一步降低,足以在3只动物中的2只预防临床综合征。2.5毫克/千克的剂量对所有动物均具有一致的保护作用。这些结果表明,丹曲林保护接触触发剂的易感动物的机制是通过降低骨骼肌细胞内的游离钙离子浓度。