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IgG4相关性硬化性胆管炎:并非总是一种明显的疾病。

IgG4-related sclerosing cholangitis: not always an obvious entity.

作者信息

Velegraki Magdalini, Vardas Emmanouil, Dervenis Christos, Fragaki Maria, Nikolaou Pinelopi, Mpitouli Afroditi, Kazamias George, Sepsa Athanasia, Giannikaki Elpida, Paspatis Gregorios A

机构信息

Department of Gastroenterology, Venizeleion General Hospital, Heraklion (Magdalini Velegraki, Emmanouil Vardas, Maria Fragaki, Pinelopi Nikolaou, Afroditi Mpitouli, Gregorios A. Paspatis).

Hepatobiliary and Pancreatic Surgery Clinic, Metropolitan Hospital, Athens (Christos Dervenis).

出版信息

Ann Gastroenterol. 2021 Jul-Aug;34(4):594-596. doi: 10.20524/aog.2021.0610. Epub 2021 Feb 26.

Abstract

Immunoglobulin G4-related sclerosing cholangitis (IgG4-SC) is a distinct type of cholangitis, currently recognized as a biliary manifestation of IgG4-related disease. We present a case of type 3 IgG4-SC in a patient with normal IgG4 serum levels, surgically treated for suspicion of cholangiocarcinoma. This case highlights that differentiating between isolated IgG4-SC and cholangiocarcinoma can present a challenging diagnostic dilemma.

摘要

免疫球蛋白G4相关性硬化性胆管炎(IgG4-SC)是一种独特类型的胆管炎,目前被认为是IgG4相关性疾病的一种胆道表现。我们报告一例血清IgG4水平正常的3型IgG4-SC患者,因怀疑胆管癌接受了手术治疗。该病例突出表明,鉴别孤立性IgG4-SC和胆管癌可能会带来具有挑战性的诊断难题。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/cb4e/8276355/e4d2a4cfa064/AnnGastroenterol-34-594-g001.jpg

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