[Mitral valve atresia with normal aortic valve and pulmonary atresia. A case with pulmonary collateral vascular perfusion by systemic pulmonary arteries].

A case of mitral atresia with normal aortic valve, situs solitus, d-loop, ASD, VSD, DORV and atresia of the pulmonary valve is presented. Systemic-pulmonary collateral arteries were the single source of collateral lung perfusion. These vessels are often found in patients with tetralogy of Fallot and pulmonary atresia with VSD. The case favours the idea that these vessels are not specific for the above mentioned cardiac anomalies. It supports the theory that they represent true embryonal vessels which can persist in cases of an inadequate or completely missing connection of the sixth aortic arch derivates with the pulmonary vascular bed.