Section of Neurosurgery, Department of Clinical Neurosciences, Foothills Medical Centre, Cumming School of Medicine, University of Calgary, Calgary, AB, Canada -
Section of Neurosurgery, Department of Clinical Neurosciences, Foothills Medical Centre, Cumming School of Medicine, University of Calgary, Calgary, AB, Canada.
J Neurosurg Sci. 2022 Oct;66(5):420-424. doi: 10.23736/S0390-5616.21.05372-8. Epub 2021 Aug 3.
Intracranial Masson tumor (intravascular papillary endothelial hyperplasia, IPEH) is a benign lesion that is thought to originate from a reactionary process in response to compromised blood flow. IPEH may be classified into one of three subtypes based on etiology as it may result from the excessive proliferation of endothelial cells within a normal vessel (primary), vascular malformation (type II), or organized hematoma (type III). We report the case of a 79-year-old woman who presented with confusion, gait instability, and urinary incontinence. Neuroimaging revealed a hemorrhagic lesion within the right lateral ventricle, which was successfully resected. To our knowledge, this is the first reported case of an intraventricular IPEH and 33 case of primary intracranial IPEH. We further performed a systematic review of the literature on all prior type I intracranial IPEH cases and discuss the importance of long-term follow-up in intracranial IPEH.
颅内 Masson 瘤（血管内乳头状内皮细胞增生症，IPEH）被认为是一种良性病变，起源于血流受限引起的反应性过程。IPEH 可能根据病因分为三种亚型，因为它可能是由于正常血管内内皮细胞过度增殖（原发性）、血管畸形（II 型）或已形成的血肿（III 型）引起的。我们报告了一例 79 岁女性患者，其表现为意识混乱、步态不稳和尿失禁。神经影像学显示右侧侧脑室有出血性病变，病变成功切除。据我们所知，这是首例报道的脑室内 IPEH 和 33 例原发性颅内 IPEH。我们进一步对所有既往 I 型颅内 IPEH 病例的文献进行了系统回顾，并讨论了颅内 IPEH 进行长期随访的重要性。
