Department of Ophthalmology and Visual Sciences, Washington University in St. Louis, St. Louis, Missouri.
Department of Pediatrics, Division of Pediatric Hematology and Oncology, Washington University School of Medicine and St. Louis Children's Hospital, St. Louis, Missouri; and.
Retin Cases Brief Rep. 2023 Jul 1;17(4):359-361. doi: 10.1097/ICB.0000000000001185.
Evans syndrome is a rare disorder characterized by autoimmune hemolytic anemia and immune thrombocytopenia. We report the first case of ophthalmic involvement in a pediatric patient with Evans syndrome, in which painless vision loss was the presenting symptom.
A 15-year-old girl presented with acute painless loss of vision in her right eye and was found to have bilateral subhyaloid hemorrhages.
She was treated with intravenous steroids and transitioned to hydroxychloroquine. Her retinal hemorrhages resolved and her vision improved.
Nontraumatic subhyaloid hemorrhage is a rare cause of vision loss in children. Evans syndrome should be considered in the differential diagnosis of such patients when hematologic abnormalities are present.
Evans 综合征是一种罕见的疾病，其特征为自身免疫性溶血性贫血和免疫性血小板减少症。我们报告首例儿科 Evans 综合征患者出现眼部受累，其首发症状为无痛性视力丧失。
一名 15 岁女孩因右眼急性无痛性视力丧失就诊，发现双眼玻璃体内下方有积血。
她接受了静脉注射类固醇治疗，并转为羟氯喹治疗。她的视网膜出血消退，视力改善。
非外伤性玻璃体内下方积血是儿童视力丧失的罕见原因。当存在血液学异常时，应考虑 Evans 综合征作为此类患者的鉴别诊断。
