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用低苯丙氨酸肽配方治疗苯丙酮尿症。一项合作研究。

Treatment of phenylketonuria with a formula consisting of low-phenylalanine peptide. A collaborative study.

作者信息

Kitagawa T, Owada M, Aoki K, Arai S, Oura T, Matsuda I, Igarashi Y, Tada K, Katayama S, Hashida W

机构信息

Department of Pediatrics, Nihon University School of Medicine, Tokyo, Japan.

出版信息

Enzyme. 1987;38(1-4):321-7. doi: 10.1159/000469222.

DOI:10.1159/000469222
PMID:3440451
Abstract

A method of preparation of a more palatable therapeutic formula for phenylketonuria (PKU), consisting of low-phenylalanine peptide (LPP), was reported. There were no adverse effects and, in fact, there was a reduced frequency of diarrhea in patients who received LPP formula for more than 6 months. The LPP formula can be used not only as a more palatable therapeutic milk for PKU, but also as an ingredient to make more palatable foods of low-phenylalanine content.

摘要

据报道,有一种制备更可口的苯丙酮尿症(PKU)治疗配方的方法,该配方由低苯丙氨酸肽(LPP)组成。没有不良反应,事实上,接受LPP配方超过6个月的患者腹泻频率降低。LPP配方不仅可以用作更可口的PKU治疗奶粉,还可以用作制作低苯丙氨酸含量更可口食物的成分。

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Treatment of phenylketonuria with a formula consisting of low-phenylalanine peptide. A collaborative study.用低苯丙氨酸肽配方治疗苯丙酮尿症。一项合作研究。
Enzyme. 1987;38(1-4):321-7. doi: 10.1159/000469222.
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Dietary treatment of PKU using a low-phenylalanine peptide milk.使用低苯丙氨酸肽奶对苯丙酮尿症进行饮食治疗。
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引用本文的文献

1
Food Regime for Phenylketonuria: Presenting Complications and Possible Solutions.苯丙酮尿症的饮食疗法:现存并发症及可能的解决方法
J Multidiscip Healthc. 2022 Jan 18;15:125-136. doi: 10.2147/JMDH.S330845. eCollection 2022.
2
Successful treatment of maternal phenylketonuria with a formula consisting of low phenylalanine peptide as a protein source.以低苯丙氨酸肽作为蛋白质来源的配方成功治疗母体苯丙酮尿症。
J Inherit Metab Dis. 1988;11(3):341-4. doi: 10.1007/BF01800389.