Department of General Surgery, North Middlesex University Hospital NHS Trust, London, UK
Department of Paediatric Surgery, Nottingham University Hospitals NHS Trust, Nottingham, UK.
BMJ Case Rep. 2021 Sep 8;14(9):e242904. doi: 10.1136/bcr-2021-242904.
A baby with an antenatal diagnosis of exomphalos was born at term. The abnormality had a highly unusual appearance, a right-sided paraumbilical defect, similar to gastroschisis, but with a sac typical of exomphalos containing both abdominal contents and over 1 L of serosanguinous fluid. The sac was drained and suspended from the top of the incubator in silo fashion. Definitive closure was achieved at day 3 of life, and the patient had a non-eventful recovery. Despite exomphalos and gastroschisis normally being discrete entities, ambiguity in the presentation this case necessitated a composite management approach.
一名经产前诊断为脐膨出的婴儿足月出生。该畸形具有非常异常的外观,右侧脐旁缺损,类似于腹裂,但有一个典型的脐膨出囊,包含腹部内容物和超过 1 升的浆液血性液体。囊被引流并以筒仓的方式悬挂在孵化器的顶部。在出生后的第 3 天完成了确定性关闭,患者恢复顺利,无并发症。尽管脐膨出和腹裂通常是不同的实体,但该病例的表现存在模糊性,需要采用综合管理方法。