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经电视胸腔镜肺活检确诊的罕见病例:弥漫性肺脑膜皮瘤病

A Rare Case Diagnosed by Videothoracoscopic Lung Biopsy: Diffuse Pulmonary Meningotheliomatosis.

作者信息

Dzian Anton, Malík Marek, Hamada Ľuboš, Mičák Jozef, Gregorová Ivana, Košturiaková Gabriela

机构信息

Department of Thoracic Surgery, Jessenius Faculty of Medicine in Martin, Comenius University in Bratislava, University Hospital in Martin, Kollárova 2, 036 59 Martin, Slovakia.

Department of Pathological Anatomy, Jessenius Faculty of Medicine in Martin, Comenius University in Bratislava, University Hospital in Martin, Kollárova 2, 036 59 Martin, Slovakia.

出版信息

Case Rep Pulmonol. 2021 Aug 28;2021:1990433. doi: 10.1155/2021/1990433. eCollection 2021.

DOI:10.1155/2021/1990433
PMID:34497730
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC8419490/
Abstract

Diffuse pulmonary meningotheliomatosis (DPM) is reported as a diffuse parenchymal lung disease characterized by disseminating small asymptomatic nodules. These lesions are often detected incidentally as microscopic findings in lung specimens or autopsies examined by a pathologist. We report a case of a 60-year-old male asymptomatic patient presenting with multiple bilateral pulmonary nodules on high-resolution computed tomography and diagnosed by videothoracoscopic surgery. Differential diagnosis of patients presenting with diffuse indeterminate nodules is very important. Definitive diagnosis of DPM requires histopathology and most often videothoracoscopic lung biopsy.

摘要

弥漫性肺脑膜瘤病(DPM)被报道为一种以弥漫性分布的小的无症状结节为特征的弥漫性实质性肺病。这些病变常在病理学家检查的肺标本或尸检中作为微观发现被偶然检测到。我们报告一例60岁男性无症状患者,其在高分辨率计算机断层扫描上表现为双侧多发肺结节,并通过电视胸腔镜手术确诊。对表现为弥漫性不确定结节的患者进行鉴别诊断非常重要。DPM的确诊需要组织病理学检查,且大多情况下需要电视胸腔镜肺活检。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9242/8419490/7f23787c6bfd/CRIPU2021-1990433.002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9242/8419490/d6e243efedf7/CRIPU2021-1990433.001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9242/8419490/7f23787c6bfd/CRIPU2021-1990433.002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9242/8419490/d6e243efedf7/CRIPU2021-1990433.001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9242/8419490/7f23787c6bfd/CRIPU2021-1990433.002.jpg

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