Shrestha Bibek Man, Shrestha Suraj, Kharel Sanjeev, K C Ajay, Shrestha Sujan, Pradhan Sumita, Bhandari Ramesh Singh
Maharajgunj Medical Campus, Institute of Medicine, Kathmandu, Nepal.
Maharajgunj Medical Campus, Institute of Medicine, Kathmandu, Nepal.
Int J Surg Case Rep. 2021 Oct;87:106409. doi: 10.1016/j.ijscr.2021.106409. Epub 2021 Sep 15.
Lupus enteritis is uncommon in patients with SLE and usually presents with anorexia, vomiting, and abdominal pain. Intestinal perforation as an initial manifestation of SLE is rare and can have a grave prognosis if not timely diagnosed.
We report an unusual case of a 22-year-old regularly menstruating female who presented with features of perforation peritonitis as an initial manifestation of lupus enteritis. Intraoperatively, a gangrenous ileal segment with multiple perforations was present. Thus, with an intraoperative diagnosis of perforation peritonitis, a gangrenous segment of the small bowel was resected and a double-barrel jejuno-ileostomy was created.
Lupus enteritis manifesting initially as bowel perforation can be an uncommon cause of acute abdomen. A plain chest X-ray can show gas under the diaphragm suggesting bowel perforation. A contrast-enhanced CT scan of the abdomen is the gold standard in diagnosing lupus enteritis with a good prognosis on steroids.
Primary closure, resection, and anastomosis of small gut or diverting stoma are required for management of perforation. A high degree of clinical suspicion is required for early diagnosis thus preventing the grave prognosis of such an entity.
狼疮性肠炎在系统性红斑狼疮患者中并不常见,通常表现为厌食、呕吐和腹痛。肠道穿孔作为系统性红斑狼疮的初始表现较为罕见,如果不及时诊断,预后可能很严重。
我们报告了一例不寻常的病例,一名22岁月经规律的女性,以穿孔性腹膜炎为狼疮性肠炎的初始表现。术中发现一段坏疽性回肠伴有多处穿孔。因此,术中诊断为穿孔性腹膜炎后,切除了一段小肠坏疽段,并进行了双腔空肠回肠造口术。
最初表现为肠穿孔的狼疮性肠炎可能是急腹症的罕见原因。胸部X线平片可显示膈下游离气体,提示肠穿孔。腹部增强CT扫描是诊断狼疮性肠炎的金标准,使用类固醇治疗预后良好。
对于穿孔的处理,需要进行小肠的一期缝合、切除和吻合或造口术。早期诊断需要高度的临床怀疑,从而防止此类疾病的严重预后。