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伴有眼部受累的水疱样疹样淋巴组织增生性疾病。

Hydroa vacciniforme-like lymphoproliferative disorder with eye involvement.

机构信息

Department of Dermatology, West China Hospital Sichuan University, Chengdu, China.

Department of Ophthalmlogy, West China Hospital Sichuan University, Chengdu, China.

出版信息

Pediatr Dermatol. 2021 Sep;38(5):1387-1388. doi: 10.1111/pde.14808. Epub 2021 Sep 24.

Abstract

Hydroa vacciniforme-like lymphoproliferative disorder (HVLPD) is characterized by vesiculopapular eruptions on sun-exposed and sometimes unexposed skin. Though ocular involvement in HVLPD is rare, it may present with conjunctivitis, corneal opacities, uveitis, and interstitial keratitis. We report a case of a 7-year-old boy with HVLPD, whose ophthalmic symptoms were neglected for over 2 years, who developed anterior uveitis and corneal nebulae without vision impairment. Awareness of eye involvement in patients with HVLPD may help to prevent severe complications.

摘要

水疱样疹样淋巴增生性疾病(HVLPD)的特征是在暴露于阳光和有时未暴露于阳光的皮肤上出现水疱性丘疹性皮疹。尽管 HVLPD 中的眼部受累很少见,但它可能表现为结膜炎、角膜混浊、葡萄膜炎和间质性角膜炎。我们报告了一例 7 岁男孩患有 HVLPD,其眼部症状被忽视了 2 年以上,他出现了前葡萄膜炎和角膜云翳,但没有视力损害。了解 HVLPD 患者的眼部受累情况可能有助于预防严重并发症。

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