Orthopaedic, Laiko General Hospital, Athens, Greece
Internal Medicine, Laiko General Hospital, Athens, Greece
BMJ Case Rep. 2021 Sep 30;14(9):e242033. doi: 10.1136/bcr-2021-242033.
We present the case of a fifteen-year-old achondroplastic (ACH) woman who requested to have her femurs lengthened by intramedullary nails. She had undergone bilateral tibial lengthening at the age of eleven and presented with a varus deformity of the right lower limb, lateral thrust of the right knee and valgus deformity of the left lower limb. We performed deformity analyses based on mechanical axis measurements, and we came with a staged surgical plan. In ACH adolescences, correction of bony deformity needs to encounter continuous fibula growth dynamics. Lateral knee thrust was corrected by gradual distal translation of the fibula head via an Ilizarov frame and the amount of translation we decided clinically. Tibial lengthening and valgus osteotomy of the distal femur accentuate lateral collateral ligament (LCL) complex laxity. In patients with ACH, tibial lengthening and valgus osteotomy of the distal femur-if needed-should precede LCL complex tightening, and femoral lengthening should follow.
我们报告了一例 15 岁的软骨发育不全(ACH)女性患者,她要求通过髓内钉延长股骨。她在 11 岁时接受了双侧胫骨延长术,目前存在右下肢内翻畸形、右膝外侧推力和左下肢外翻畸形。我们根据机械轴测量进行了畸形分析,并制定了分期手术计划。在 ACH 青少年中,矫正骨畸形需要应对腓骨持续生长的动态变化。通过 Ilizarov 框架和我们临床决定的翻译量,逐渐将腓骨头向远端平移来矫正外侧膝推力。胫骨延长和股骨远端的外翻截骨术加重了外侧副韧带(LCL)复合体的松弛。在 ACH 患者中,如果需要,胫骨延长和股骨远端的外翻截骨术应先于 LCL 复合体收紧,然后再进行股骨延长。