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围手术期和并发症管理在使用静脉-动脉体外膜肺氧合(V-A ECMO)治疗嗜铬细胞瘤危象中的重要性:病例报告及文献复习。

The importance of perioperative and complication management in the treatment of pheochromocytoma crisis with venoarterial extracorporeal membrane oxygenation (V-A ECMO): a case report and review of the literature.

机构信息

Hangzhou Geriatric Hospital, Hangzhou First People's Hospital Group, Hangzhou, China.

Affiliated Hangzhou First People's Hospital, Zhejiang University School of Medicine, Hangzhou, China.

出版信息

Perfusion. 2023 Mar;38(2):228-235. doi: 10.1177/02676591211049314. Epub 2021 Oct 7.

DOI:10.1177/02676591211049314
PMID:34617860
Abstract

PURPOSE

In this article, we aimed to elaborate on perioperative and complication management in treatment of pheochromocytoma crisis with extracorporeal membrane oxygenation (ECMO).

MATERIAL AND METHODS

We report a case of relatively rare grant paraganglioma-induced pheochromocytoma crisis leading to severe circulatory failure, treated with venoarterial extracorporeal membrane oxygenation (V-A ECMO) as a bridge to curative adrenalectomy. Weaning of ECMO was followed by successful surgical removal of the tumor, and patient survival. However, distal ischemia of the cannulated leg occurred during ECMO operation, which eventually led to amputation. In addition, the patient developed new cerebral infarction and left hemiplegia, half a month after paraganglioma resection.

CONCLUSIONS

We believe that patients with pheochromocytoma crisis, who cannot maintain blood circulation, are eligible for V-A ECMO treatment. Moreover, care should be taken to prevent thrombosis and individualized and precise blood pressure management targets. Early detection and treatment of thrombosis is imperative to long-term prognosis of patients with ECMO.

摘要

目的

本文旨在阐述体外膜肺氧合(ECMO)在治疗嗜铬细胞瘤危象中的围手术期和并发症管理。

材料与方法

我们报告了一例罕见的格兰特副神经节瘤引起的嗜铬细胞瘤危象导致严重循环衰竭,通过静脉-动脉体外膜肺氧合(V-A ECMO)作为桥接治疗性肾上腺切除术。ECMO 脱机后成功切除肿瘤,患者存活。然而,在 ECMO 手术过程中出现了插管腿的远端缺血,最终导致截肢。此外,在副神经节瘤切除后半个月,患者出现新的脑梗死和左侧偏瘫。

结论

我们认为不能维持血液循环的嗜铬细胞瘤危象患者适合 V-A ECMO 治疗。此外,应注意预防血栓形成,并制定个体化和精确的血压管理目标。早期发现和治疗血栓形成对于 ECMO 患者的长期预后至关重要。

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J Clin Med. 2025 Aug 20;14(16):5882. doi: 10.3390/jcm14165882.
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ECMO-Assisted Da Vinci Robotic Surgery for Pheochromocytoma-Induced Acute Catecholamine Cardiomyopathy: A Case Report.体外膜肺氧合辅助达芬奇机器人手术治疗嗜铬细胞瘤诱发的急性儿茶酚胺心肌病:一例报告
Clin Case Rep. 2025 Aug 5;13(8):e70712. doi: 10.1002/ccr3.70712. eCollection 2025 Aug.
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Risk factors for bleeding and thrombotic complications during extracorporeal membrane oxygenation support in adults based on the MIMIC-IV database.
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Surgical anesthesia in a patient with a pheochromocytoma crisis supported by ECMO: a case report.体外膜肺氧合(ECMO)支持下嗜铬细胞瘤危象患者的手术麻醉:一例报告
J Cardiothorac Surg. 2024 Dec 20;19(1):674. doi: 10.1186/s13019-024-03177-w.
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Paraganglioma-induced pheochromocytoma crisis successfully treated by veno-arterial extracorporeal membrane oxygenation: a case report.血管-动脉体外膜肺氧合成功治疗副神经节瘤诱导的嗜铬细胞瘤危象:病例报告。
J Int Med Res. 2024 Sep;52(9):3000605241270655. doi: 10.1177/03000605241270655.
6
Pheochromocytoma crisis with refractory Acute Respiratory Distress Syndrome (ARDS), Takotsubo syndrome, emergency adrenalectomy, and need for Extracorporeal Membrane Oxygenation (ECMO) in a previously undiagnosed and asymptomatic patient, due to the use of metoclopramide.由于使用了甲氧氯普胺,一位此前未被诊断且无症状的患者出现了嗜铬细胞瘤危象伴难治性急性呼吸窘迫综合征(ARDS)、心尖球形综合征、紧急肾上腺切除术和需要体外膜氧合(ECMO)。
BMC Endocr Disord. 2023 Jul 10;23(1):145. doi: 10.1186/s12902-023-01404-4.