Departamento de Oftalmología, Hospital Ángeles, Torreón (Coahuila), Mexico.
Instituto de Oftalmología Conde de Valenciana, Ciudad de México, Mexico.
Arch Soc Esp Oftalmol (Engl Ed). 2021 Oct;96(10):552-555. doi: 10.1016/j.oftale.2020.09.005. Epub 2021 Jan 6.
Of the head and neck tumoral lesions in children and adolescents, 5%-10% are primary malignant tumors. Among these tumors, orbital rhabdomyosarcoma stands out, which is the most common primary soft tissue sarcoma in children. Its diagnosis requires a high degree of clinical suspicion, and it can be corroborated with a series of examinations, in order to stage it and carry out the appropriate treatment. Currently, surgery and chemotherapy are the primary treatments, and the use of conventional radiotherapy is limited to cases where previous treatments fail or there is a risk of recurrence. The following case report aims to expose the clinical picture, diagnosis, staging and integral treatment of orbital rhabdomyosarcoma, as well as the interdisciplinary management that was performed to improve the patient's prognosis.
在儿童和青少年的头颈部肿瘤病变中,有 5%-10%是原发性恶性肿瘤。在这些肿瘤中,眼眶横纹肌肉瘤较为突出,它是儿童中最常见的原发性软组织肉瘤。其诊断需要高度的临床怀疑,并且可以通过一系列检查来证实,以便对其进行分期并进行适当的治疗。目前,手术和化疗是主要的治疗方法,常规放疗的应用仅限于先前治疗失败或存在复发风险的情况下。以下病例报告旨在揭示眼眶横纹肌肉瘤的临床特征、诊断、分期和整体治疗,以及为改善患者预后而进行的跨学科管理。