Anjana J S, Rema P, Suchetha S, Ranjith J Siva, Rao Amrita B, Preethi T R
Division of Gynecological Oncology, Regional Cancer Centre, Thiruvananthapuram, Kerala India.
Division of Surgical Oncology, Regional Cancer Centre, Thiruvananthapuram, Kerala India.
Indian J Surg Oncol. 2021 Sep;12(3):524-529. doi: 10.1007/s13193-021-01366-w. Epub 2021 Jun 5.
Extramammary Paget's disease is a rare neoplasm that may affect the vulva. It usually presents as a pruritic red eczematous lesion with islands of hyperkeratosis that is often mistaken for other benign conditions. There are no specific guidelines for the management of this disease. Surgical excision is the standard treatment but recurrences are common in spite of extensive surgery with negative margins. We report here a series of 7 cases of Paget's disease vulva treated by primary surgery. The series highlights some of the challenges in the diagnosis and management of Paget's disease vulva.
乳房外佩吉特病是一种可能累及外阴的罕见肿瘤。它通常表现为瘙痒性红色湿疹样病变,伴有角化过度岛,常被误诊为其他良性疾病。对于这种疾病的治疗没有具体的指南。手术切除是标准治疗方法,但尽管进行了广泛的手术且切缘阴性,复发仍很常见。我们在此报告一系列7例原发性手术治疗的外阴佩吉特病病例。该系列突出了外阴佩吉特病诊断和治疗中的一些挑战。