Gbenou Antoine Séraphin, Bata Abdel-Kémal Bori, Akodjènou Joseph, Zoumènou Eugène, Fiogbe Armand Michel, Tristan Jose Uroz
Service de Chirurgie Pédiatrique du Centre Hospitalier Universitaire de la Mère et de l´Enfant-Lagune, 01 BP 107, Ave Delorme, Cotonou, Bénin.
Service d'Anesthésie-Réanimation du Centre Hospitalier Universitaire de la Mère et de l´Enfant-Lagune, 01 BP 107, Ave Delorme, Cotonou, Bénin.
Pan Afr Med J. 2021 Aug 11;39:233. doi: 10.11604/pamj.2021.39.233.25646. eCollection 2021.
Sternal agenesis as well as ectopia cordis are extremely rare congenital malformations. We here report a single case treated in the Department of Paediatric Surgery in Benin. The study involved a 3-year-old girl with congenital sternal agenesis associated with ectopia cordis; firstly, she underwent controlled healing. Then thoracoplasty was performed with favourable outcome. Long-term results are good. Now, she is 13 years old, is attending school and has a satisfactory clinical condition. This is one of the few cases reported in the literature. Optimal therapeutic management has been keeping the patient alive in West Africa.
胸骨发育不全以及心脏异位是极其罕见的先天性畸形。我们在此报告一例在贝宁儿科外科治疗的病例。该研究涉及一名3岁女孩,患有先天性胸骨发育不全并伴有心脏异位;首先,她接受了控制性愈合。然后进行了胸廓成形术,效果良好。长期结果良好。现在,她13岁,正在上学,临床状况令人满意。这是文献中报道的少数病例之一。在西非,最佳的治疗管理使患者存活了下来。