Pius Simon, Abubakar Ibrahim Halima, Bello Mustapha, Bashir Tahir Mohammed
Department of Paediatrics, University of Maiduguri Teaching Hospital, Maiduguri, Nigeria.
Department of Surgery, University of Maiduguri Teaching Hospital, Maiduguri, Nigeria.
Case Rep Pediatr. 2017;2017:1858621. doi: 10.1155/2017/1858621. Epub 2017 Apr 19.
Ectopia cordis is a congenital heart exposure defined as complete or partial protrusion of heart through ventral defect in the thoracoabdominal wall alone or with other viscera in cases of pentalogy of Cantrell. This condition was first described by Haller et al. in 1706; since then many advances have been made. Diagnosis of ectopia cordis is done prenatally in well-equipped health facility by antenatal ultrasound scan so that early diagnosis and management plan can be initiated. The index case was delivered to uneducated rural family and admitted at 3 days of life and survived for seven days, even though most literatures state that majority died within four days even with surgery. So, in view of this, we presented this case report to deliberately draw the attention of paediatrician/obstetrician to the fact that even though this condition is rare, proactive search and diagnosis should be made and early treatment should be instituted, so that such a child may be salvaged.
心脏异位是一种先天性心脏暴露,定义为心脏单独通过胸腹壁的腹侧缺损完全或部分突出,或者在坎特雷尔五联症的情况下与其他内脏一起突出。这种情况最早由哈勒等人于1706年描述;从那时起已经取得了许多进展。心脏异位的诊断在设备完善的医疗机构中通过产前超声扫描在产前进行,以便启动早期诊断和管理计划。该索引病例出生于一个未受过教育的农村家庭,出生3天后入院,存活了7天,尽管大多数文献表明,即使进行手术,大多数患者也会在4天内死亡。因此,鉴于此,我们提交了这份病例报告,特意提请儿科医生/产科医生注意,尽管这种情况很少见,但仍应积极进行检查和诊断,并尽早进行治疗,以便挽救这样的患儿。