肝上皮样血管内皮细胞瘤以门静脉高压为罕见表现：病例报告。

Portal hypertension as an uncommon presentation of hepatic epithelioid hemangioendothelioma: a case report.

机构信息

Servicio de Gastroenterología, Hospital III Emergencias Grau. Lima, Perú.

Servicio de Patología Quirúrgica y Necropsias, Hospital Nacional Guillermo Almenara Irigoyen. Lima, Perú.

出版信息

Rev Gastroenterol Peru. 2021 Apr-Jun;41(2):103-106.

Abstract

Hepatic epithelioid hemangioendothelioma (HEHE) is a vascular tumor with a low incidence rate. We report a case of a 26-year-old man who was referred to our hospital with a misdiagnosis of liver cirrhosis. On physical examination, ascites was noted. Chest and abdominal computer tomography scans showed coalescent lesions involving the peripheral liver with heterogeneous contrast enhancement and portal vein dilation due to portal hypertension. Extrahepatic metastasis was not observed. The biopsy with immunohistochemical stains suggested HEHE (Factor VIII, CD31, and CD34). This report describes an uncommon case of HEHE with non-cirrhotic portal hypertension.

摘要

肝上皮样血管内皮细胞瘤（HEHE）是一种发病率较低的血管肿瘤。我们报告了 1 例 26 岁男性患者，因误诊为肝硬化而被转至我院。体格检查时发现腹水。胸部和腹部计算机断层扫描显示融合性病变累及外周肝脏，伴有不均匀的对比增强，由于门静脉高压导致门静脉扩张。未观察到肝外转移。免疫组织化学染色活检提示 HEHE（VIII 因子、CD31 和 CD34）。本报告描述了 1 例非肝硬化性门静脉高压症的不常见 HEHE 病例。