Department of Obstetrics and Gynecology, Peking Union Medical College Hospital, Chinese Academy of Medical Sciences, National Clinical Research Center for Obstetrical and Gynecological Diseases, State Key Laboratory of Complex Severe and Rare Diseases (Peking Union Medical College Hospital), Beijing, China.
Department of Obstetrics and Gynecology, Peking Union Medical College Hospital, Chinese Academy of Medical Sciences, National Clinical Research Center for Obstetrical and Gynecological Diseases, State Key Laboratory of Complex Severe and Rare Diseases (Peking Union Medical College Hospital), Beijing, China; Peking Union Medical College, M.D. Program, Department of Obstetrics and Gynecology, Peking Union Medical College Hospital, Dongcheng District, Beijing, China.
J Pediatr Adolesc Gynecol. 2022 Jun;35(3):396-399. doi: 10.1016/j.jpag.2021.10.014. Epub 2021 Nov 4.
Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome, as congenital anomaly of the female reproductive tract, is characterized by the congenital absence of uterus and vagina. Dilation maneuver was recommended as the nonsurgical treatment for these patients. However, only several cases were reported depicting the prolapse of the dilated neovagina of patients with MRKH syndrome.
We report our own experiences in treating 2 patients with neovaginal prolapse MRKH syndrome receiving ischial spinous fascia fixation (ISFF) and reviewed neovaginal prolapse occurrence in MRKH syndrome. In our approach to evaluating the anatomic and functional outcome after operation, we compared the prolapse stage with Pelvic Organ Prolapse Quantification score and analyzed sexual activities by the standardized Female Sexual Function Index (FSFI) and Modified Body Image Scale (MBIS).
Both subjective and objective improvement were observed in these 2 patients.
Mayer-Rokitansky-Küster-Hauser（MRKH）综合征是一种女性生殖道先天性异常，其特征为先天性子宫和阴道缺失。扩张术被推荐作为这些患者的非手术治疗方法。然而，只有少数几例报道描述了 MRKH 综合征患者扩张的新阴道脱垂。
我们报告了 2 例接受坐骨棘筋膜固定术（ISFF）的 MRKH 综合征新阴道脱垂患者的自身经验，并回顾了 MRKH 综合征中新阴道脱垂的发生情况。在评估手术前后解剖和功能结果时，我们将脱垂阶段与盆腔器官脱垂定量（POP-Q）评分进行了比较，并使用标准化的女性性功能指数（FSFI）和改良身体意象量表（MBIS）分析了性行为。
这 2 例患者均观察到主观和客观改善。
