Department of Neurosurgery, PGIMER, Chandigarh, India.
Department of Neurosurgery, KGMU, Lucknow, Uttar Pradesh, India.
Neurol India. 2021 Sep-Oct;69(5):1405-1408. doi: 10.4103/0028-3886.329577.
Extraosseous primary spinal intradural Ewing's sarcoma (ES) is an unusual entity. Bleed within such tumors with acute neurological worsening is extremely rare, especially in the pediatric age. In this article, we present two children with intradural-extramedullary ES who had sudden decline in their neurological status consequent to an intratumoral hemorrhage. We discuss their clinical course and also briefly review the pertinent literature. Spinal intradural Ewing's sarcomas possibly have a tendency to bleed. A short clinical symptomatology along with an acute neurological deterioration and radiologic evidence of intratumoral hemorrhage in a spinal intradural tumor should raise the suspicion of an ES.
骨外原发性脊髓硬膜内尤文肉瘤（ES）是一种不常见的实体瘤。此类肿瘤内出血伴急性神经恶化极为罕见，尤其是在儿科。本文报道了 2 例硬膜内-髓外 ES 患儿，因肿瘤内出血导致神经状态突然下降。我们讨论了他们的临床过程，并简要回顾了相关文献。脊髓硬膜内尤文肉瘤可能有出血倾向。在脊髓硬膜内肿瘤中，伴有短时间临床症状、急性神经恶化和肿瘤内出血的放射学证据，应提示 ES 的可能。
