Ma Kai-Ge, Hu Hai-Bo, Zhou Jin-Song, Ji Chao, Yan Qi-Sheng, Peng Si-Ming, Ren Lan-Dong, Yang Bing-Nan, Xiao Xin-Li, Ma Yan-Bing, Wu Feng, Si Kai-Wei, Wu Xiao-Lin, Liu Jian-Xin
Institute of Neurobiology, School of Basic Medical Sciences, Xi'an Jiaotong University Health Science Center, 76 West Yanta Road, Xi'an 710061, China.
Department of Human Anatomy, Histology and Embryology, School of Basic Medical Sciences, Xi'an Jiaotong University Health Science Center, 76 West Yanta Road, Xi'an 710061, China.
Exp Neurol. 2022 Jan;347:113918. doi: 10.1016/j.expneurol.2021.113918. Epub 2021 Nov 5.
In temporal lobe epilepsy (TLE), abnormal axon guidance and synapse formation lead to sprouting of mossy fibers in the hippocampus, which is one of the most consistent pathological findings in patients and animal models with TLE. Glypican 4 (Gpc4) belongs to the heparan sulfate proteoglycan family, which play an important role in axon guidance and excitatory synapse formation. However, the role of Gpc4 in the development of mossy fibers sprouting (MFS) and its underlying mechanism remain unknown. Using a pilocarpine-induced mice model of epilepsy, we showed that Gpc4 expression was significantly increased in the stratum granulosum of the dentate gyrus at 1 week after status epilepticus (SE). Using Gpc4 overexpression or Gpc4 shRNA lentivirus to regulate the Gpc4 level in the dentate gyrus, increased or decreased levels of netrin-1, SynI, PSD-95, and Timm score were observed in the dentate gyrus, indicating a crucial role of Gpc4 in modulating the development of functional MFS. The observed effects of Gpc4 on MFS were significantly antagonized when mice were treated with L-leucine or rapamycin, an agonist or antagonist of the mammalian target of rapamycin (mTOR) signal, respectively, demonstrating that mTOR pathway is an essential requirement for Gpc4-regulated MFS. Additionally, the attenuated spontaneous recurrent seizures (SRSs) were observed during chronic stage of the disease by suppressing the Gpc4 expression after SE. Altogether, our findings demonstrate a novel control of neuronal Gpc4 on the development of MFS through the mTOR pathway after pilocarpine-induced SE. Our results also strongly suggest that Gpc4 may serve as a promising target for antiepileptic studies.
在颞叶癫痫(TLE)中,异常的轴突导向和突触形成导致海马中苔藓纤维的发芽,这是TLE患者和动物模型中最一致的病理发现之一。磷脂酰肌醇蛋白聚糖4(Gpc4)属于硫酸乙酰肝素蛋白聚糖家族,在轴突导向和兴奋性突触形成中起重要作用。然而,Gpc4在苔藓纤维发芽(MFS)发展中的作用及其潜在机制仍不清楚。使用毛果芸香碱诱导的癫痫小鼠模型,我们发现癫痫持续状态(SE)后1周,齿状回颗粒层中Gpc4表达显著增加。使用Gpc4过表达或Gpc4 shRNA慢病毒调节齿状回中的Gpc4水平,在齿状回中观察到netrin-1、SynI、PSD-95和Timm评分水平的升高或降低,表明Gpc4在调节功能性MFS的发展中起关键作用。当分别用L-亮氨酸或雷帕霉素(哺乳动物雷帕霉素靶蛋白(mTOR)信号的激动剂或拮抗剂)处理小鼠时,观察到Gpc4对MFS的影响被显著拮抗,这表明mTOR通路是Gpc4调节MFS所必需的。此外,在疾病慢性期通过抑制SE后的Gpc4表达,观察到自发性反复癫痫发作(SRSs)减弱。总之,我们的研究结果表明,在毛果芸香碱诱导的SE后,神经元Gpc4通过mTOR通路对MFS的发展具有新的调控作用。我们的结果还强烈表明,Gpc4可能是抗癫痫研究的一个有前途的靶点。